Cardiology in the Young ( IF 0.9 ) Pub Date : 2022-08-15 , DOI: 10.1017/s1047951122002268 Trisha V Vigneswaran 1 , Lindsey E Hunter 2 , Julene S Carvalho 3, 4, 5 , Anna N Seale 6, 7
To investigate UK variability in prenatal and postnatal management strategy of right aortic arch and double aortic arch (RAA/DAA).
Methods:Online surveys were sent to senior physicians (consultants) of the National Fetal Cardiology Working Group regarding prenatal diagnosis, counselling, and perinatal management of antenatally diagnosed RAA/DAA and to the British Congenital Cardiovascular Association regarding postnatal management strategies.
Results:There were 28 prenatal and 90 postnatal surveys completed. Prenatally, there was consensus for potential associated chromosomal/genetic anomalies, but there was variation in the risk quoted. Confidence in defining aortic arch morphology was reported by 43% (12/28) of fetal cardiologists. There was variation in what was felt to be possible symptoms/signs of a compressive vascular ring, postnatal investigation, postnatal management, follow-up duration of asymptomatic patients, and indications for surgical intervention.
Conclusion:This study has highlighted important areas for future research: improving accuracy of prenatal diagnosis, clarification of potential symptoms, optimal investigation strategies, and indications for surgery.
中文翻译:
产前检测到的血管环的管理:英国全国调查
客观的:
旨在调查英国右主动脉弓和双主动脉弓 (RAA/DAA) 产前和产后管理策略的差异。
方法:我们向国家胎儿心脏病学工作组的高级医生(顾问)发送了有关产前诊断 RAA/DAA 的产前诊断、咨询和围产期管理的在线调查,并向英国先天性心血管协会发送了有关产后管理策略的在线调查。
结果:已完成 28 项产前调查和 90 项产后调查。产前,对于潜在的相关染色体/遗传异常存在共识,但所引用的风险存在差异。43% (12/28) 的胎儿心脏病专家报告对定义主动脉弓形态有信心。受压血管环的可能症状/体征、产后检查、产后管理、无症状患者的随访时间以及手术干预的指征存在差异。
结论:这项研究强调了未来研究的重要领域:提高产前诊断的准确性、澄清潜在症状、最佳检查策略和手术指征。