Abstract

Background: Unroofed coronary sinus is a congenital cardiac anomaly usually associated with persistent left superior vena cava. Premature restriction or closure of foramen ovale is described in association with hypoplastic left heart syndrome. Abdominal peritoneal bands when present manifest clinically. Case report: A 27 years, gravida 2, presented with intrauterine fetal death at 24 weeks gestation due to fetal congestive cardiac failure, cardiomegaly and hydrops. Perinatal autopsy showed absent coronary sinus with cardiac veins draining directly into the heart. There was no persistent left superior vena cava. The foramen ovale was restricted prematurely. The ductus arteriosus was present and non-restrictive. Abdomen showed a cysto-colic peritoneal band. Conclusion: This is the first report showing a triad of (1) complete absence of coronary sinus without left superior vena cava (type-II); (2) premature restriction of foramen ovale without hypoplastic left heart; and (3) a cysto-colic peritoneal band between the gall bladder and colon.

摘要

背景：无顶冠状窦是一种先天性心脏异常，通常与持续存在的左上腔静脉有关。卵圆孔过早受限或闭合与左心发育不全综合征有关。腹部腹膜带在临床上表现出来。病例报告：一名 27 岁的孕妇 2 岁，因胎儿充血性心力衰竭、心脏肥大和积水而在妊娠 24 周时出现宫内死胎。围产期尸检显示没有冠状窦，心脏静脉直接流入心脏。没有持续存在的左上腔静脉。卵圆孔过早受限。动脉导管存在且非限制性。腹部显示膀胱绞痛腹膜带。结论：这是第一份显示三联征的报告：（1）冠状窦完全缺失，无左上腔静脉（II 型）；(2)无左心发育不全的卵圆孔过早受限；(3) 胆囊和结肠之间的膀胱绞痛腹膜带。