Background

Because of sports and exercise restrictions, children with inherited cardiac disease are at risk of physical deconditioning. Guidelines on sports participation in cardiovascular disease have become less restrictive over time, but their real-life application and behavioural impact have seldom been evaluated in children.

Aims

We aimed to evaluate adherence to the 2020 European Society of Cardiology guidelines on sports and exercise in children with inherited cardiac arrhythmia and inherited cardiomyopathy; we also sought to evaluate their aerobic fitness, and the behavioural impact of inherited cardiac diseases on physical activity in children.

Methods

Children aged 6–18 years with inherited cardiomyopathy or inherited cardiac arrhythmia were eligible for this cross-sectional study. Clinical, demographic and qualitative data were analysed.

Results

A total of 32 children were included in the study (mean age 12.7 ± 3.5 years). Most children (81.3%) complied with the 2020 European Society of Cardiology guidelines; they were physically active and had good overall aerobic fitness, with a mean peak oxygen uptake (VO₂) value of 36.5 ± 8.0 mL/kg/min (84.0 ± 17.2% of theoretical value). As a result of personal or parental behaviour, some children at risk of sudden cardiac death did not comply with the recommended upper limit of physical activity intensity, whereas others at low risk did not comply with the lower limit.

Conclusion

Most children with inherited cardiac arrhythmia or inherited cardiomyopathy complied with current 2020 European Society of Cardiology guidelines on sports cardiology and exercise in cardiovascular disease.

中文翻译：

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遗传性心脏病儿童的体力活动和有氧运动

背景

由于运动和锻炼的限制，患有遗传性心脏病的儿童面临身体状况不佳的风险。随着时间的推移，关于运动参与心血管疾病的指南的限制越来越少，但它们在现实生活中的应用和行为影响很少在儿童中得到评估。

宗旨

我们旨在评估对 2020 年欧洲心脏病学会关于遗传性心律失常和遗传性心肌病儿童运动和锻炼指南的依从性；我们还试图评估他们的有氧健康状况，以及遗传性心脏病对儿童身体活动的行为影响。

方法

患有遗传性心肌病或遗传性心律失常的 6-18 岁儿童符合这项横断面研究的条件。分析了临床、人口统计学和定性数据。

结果

该研究共包括 32 名儿童（平均年龄 12.7  ±  3.5 岁）。大多数儿童 (81.3%) 遵守了 2020 年欧洲心脏病学会指南；他们身体活跃，整体有氧健康状况良好，平均峰值摄氧量 (VO ₂ ) 值为 36.5  ±  8.0  mL/kg/min（理论值的84.0  ±  17.2%）。由于个人或父母的行为，一些有心脏性猝死风险的儿童没有遵守推荐的体力活动强度上限，而其他低风险的儿童没有遵守下限。

结论

大多数患有遗传性心律失常或遗传性心肌病的儿童都遵守了 2020 年欧洲心脏病学会关于运动心脏病学和心血管疾病运动的现行指南。