Abstract

Pericardial agenesis is a rarely seen congenital defect characterised by the partial or, more rarely complete, absence of the pericardium. Most often asymptomatic, it is usually incidentally discovered following the demonstration of heart’s laevorotation on imaging, in the operating room or at autopsy. In this article, we report the case of an 80-year-old patient with asymptomatic complete pericardial agenesis fortuitous discovered. Pericardial agenesis observations are extremely uncommon reported in the literature, which substantiate its original epidemiological character. In addition, this observation brings some clinical, electrical as well as iconographic elements to better understand the pathology and raises clinical suspicions. Finally, this case report confirms the exceptionally symptomatic nature of the pathology, illustrating the irrelevance of treatment or specific follow-up.

摘要

心包发育不全是一种罕见的先天性缺陷，其特征是心包部分缺失，或更罕见的是完全缺失。大多数情况下是无症状的，通常是在手术室或尸检中通过影像学证明心脏左旋后偶然发现的。在本文中，我们报道了一位偶然发现的无症状完全性心包发育不全的80岁患者的病例。文献报道心包发育不全的现象极为罕见，这证实了其最初的流行病学特征。此外，这一观察结果还带来了一些临床、电学和图像元素，以更好地了解病理学并提出临床怀疑。最后，本病例报告证实了病理学的异常症状性质，