Despite acceptable survival for Fontan operation, there are concerns about late complications affecting the major organs. We herein present two cases of adults after Fontan operation who developed focal segmental glomerulosclerosis. These cases suggest that focal segmental glomerulosclerosis is owing to haemodynamic incompetence associated with Fontan operation, including congestion, hypoxia, and hyperviscosity, which may be called Fontan-associated renal disease.

中文翻译：

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Fontan 手术后患者的局灶节段性肾小球硬化：这是与 Fontan 相关的肾脏疾病吗？

尽管 Fontan 手术的存活率可以接受，但人们担心晚期并发症会影响主要器官。我们在此介绍了两例 Fontan 手术后发生局灶节段性肾小球硬化的成人病例。这些病例表明局灶节段性肾小球硬化是由于与 Fontan 手术相关的血流动力学功能障碍，包括充血、缺氧和高粘滞性，可称为 Fontan 相关肾病。