Combined tricuspid atresia and absent pulmonary valve with dysplasia of the right ventricular myocardium is a very rare congenital heart anomaly with a poor prognosis. We present three cases of this rare disease that reached the Fontan operation without prior surgical intervention of the right ventricle or pulmonary artery; no right ventriclar dilation was detected. All patients had uneventful post-operative courses.

中文翻译：

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Fontan 手术治疗三尖瓣闭锁伴肺动脉瓣缺失：病例系列

三尖瓣闭锁和肺动脉瓣缺如合并右心室心肌发育不良是一种非常罕见的先天性心脏异常，预后较差。我们介绍了三例这种罕见疾病，它们在没有事先对右心室或肺动脉进行手术干预的情况下进行了 Fontan 手术；未检测到右心室扩张。所有患者的术后过程都很顺利。