Congenital portosystemic shunts (CPSS) may produce a variety of severe, clinically detrimental presentations. When indicated, closure is recommended; however, if the intrahepatic portal venous system (IPVS) is underdeveloped complete closure may not be possible and may result in severe acute portal hypertension. Staged restriction of CPSS flow by both surgical and complex transcatheter interventions has been successful in augmenting development of the IPVS such that complete occlusion of the CPSS can be performed. We report use of a modified microvascular plug to restrict CPSS flow with subsequent IPVS development and safe complete occlusion of CPSS.

中文翻译：

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改良微血管栓塞限制先天性门体分流术

先天性门体分流术 (CPSS) 可能会产生多种严重的、对临床有害的表现。当有指示时，建议关闭；然而，如果肝内门静脉系统 (IPVS) 发育不良，则可能无法完全闭合，并可能导致严重的急性门静脉高压。通过手术和复杂的经导管干预对 CPSS 流量进行分阶段限制已成功地促进了 IPVS 的发展，从而可以实现 CPSS 的完全闭塞。我们报告使用改良的微血管塞来限制 CPSS 流量，随后 IPVS 发展和 CPSS 的安全完全闭塞。