Exercise is considered as an important component of the package of care delivered to people with cystic fibrosis (pwCF). However, despite the well-known short-term physiological and psychological benefits, training effects are heterogenous and the transfer of structured exercise programmes to the daily life of pwCF is challenging. Training concepts and strategies developed over the last decades must be adapted to consider the aging population of pwCF with associated comorbidities, and also a new generation of young pwCF that are healthier than ever. In the present review we propose a new framework for optimising the choice among available exercise training procedures and we provide a theoretical and scientifically justified rationale for considering and testing new exercise training modalities. We propose a multidisciplinary approach, considering various physiological, psychological and logistical factors, with the aim to increase effects of exercise training and build positive long-term exercise behaviour.

运动被认为是囊性纤维化 (pwCF) 患者一揽子护理的重要组成部分。然而，尽管众所周知的短期生理和心理益处，但训练效果是异质的，将结构化锻炼计划转移到 pwCF 的日常生活中具有挑战性。过去几十年发展起来的培训理念和策略必须适应 pwCF 的老龄化人口和相关合并症，以及比以往任何时候都更健康的新一代年轻 pwCF。在本次审查中，我们提出了一个新的框架，用于优化现有运动训练程序的选择，并为考虑和测试新的运动训练方式提供了理论和科学合理的理由。我们提出了一种多学科的方法，