Neurocutaneous melanocytosis (NCM) is characterized by melanocyte deposition in the leptomeninges and brain parenchyma, primarily occurring in children with large or giant congenital melanocytic nevi (LCMN) or multiple congenital melanocytic nevi. Patients with NCM may develop hydrocephalus and increased intracranial pressure, which can be managed with ventriculoperitoneal (VP) shunting. We present the case of a 16-month-old girl who developed peritoneal carcinomatosis and malignant ascites following VP shunting for hydrocephalus secondary to NCM to increase awareness of this rare, but serious, complication of cerebrospinal fluid diversion.

中文翻译：

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表现为腹膜种植的神经皮肤黑色素细胞增多症相关的恶性黑色素瘤

神经皮肤黑色素细胞增多症 (NCM) 的特征是黑色素细胞沉积在软脑膜和脑实质中，主要发生在患有大型或巨大先天性黑色素细胞痣 (LCMN) 或多发性先天性黑色素细胞痣的儿童中。NCM 患者可能出现脑积水和颅内压升高，可以通过脑室腹腔 (VP) 分流术进行管理。我们介绍了一例 16 个月大的女孩，她因继发于 NCM 的脑积水进行 VP 分流后出现腹膜癌病和恶性腹水，以提高对这种罕见但严重的脑脊液分流并发症的认识。