Background: Annual in-hospital respiratory evaluations (AREs) during wakefulness and sleep are recommended to assess ventilatory requirements in patients with congenital central hypoventilation syndrome (CCHS) aged ≥2–3 years based on expert consensus. This study aimed to determine if AREs in patients with CCHS led to changes in ventilatory management.

中文翻译：

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先天性中枢性通气不足综合征的年度呼吸评估和通气管理的变化

背景：根据专家共识，建议在清醒和睡眠期间每年进行一次院内呼吸评估 (AREs)，以评估年龄≥2-3 岁的先天性中枢性低通气综合征 (CCHS) 患者的通气需求。本研究旨在确定 CCHS 患者的 ARE 是否会导致通气管理的改变。