Solitary fibrous tumors (SFTs), an uncommon subtype of soft tissue sarcomas mesenchymal, are frequently diagnosed in the intra-thoracic region. Distant metastasis is detected in 10-40% of SFT patients with a predilection site to the lungs; nevertheless, these can occur rarely in the liver, brain, and bones. This entity was also reported in the abdomen, trunk, head, and neck, extremities but also, in the central nervous system (CNS). In the latter form of SFTs, the meninges were mostly affected while only a few cases were reported in the intraventricular and intraparenchymal region with distinct clinical and behavioral characteristics. In this article, we report the rare case of a relapsing intraventricular SFT with secondary extra-cranial metastases to the bones and soft tissues after 11 years of initial diagnosis, with focus on the available data in the literature on CNS SFTs.

中文翻译：

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脑室内孤立性纤维瘤长期颅外转移复发：病例报告。

孤立性纤维瘤（SFT）是间质性软组织肉瘤的一种罕见亚型，经常在胸腔内诊断。10-40% 的 SFT 患者检测到远处转移，好发部位为肺部；然而，这些情况很少发生在肝脏、大脑和骨骼中。据报道，该实体也出现在腹部、躯干、头部、颈部、四肢以及中枢神经系统（CNS）中。在后一种形式的 SFT 中，脑膜主要受到影响，而脑室内和实质内区域仅报告少数病例，具有独特的临床和行为特征。在本文中，我们报告了罕见的复发性脑室内 SFT 病例，该病例在初次诊断 11 年后继发颅外骨和软组织转移，重点关注 CNS SFT 文献中的现有数据。