当前位置: X-MOL 学术Neurology › 论文详情
Our official English website, www.x-mol.net, welcomes your feedback! (Note: you will need to create a separate account there.)
Teaching NeuroImage: Basal Ganglia T1 Hyperintensity and SWI Signal Diabetic Striatopathy in an 18-Year-Old Man With Type 1 Diabetes Mellitus
Neurology ( IF 7.7 ) Pub Date : 2021-11-23 , DOI: 10.1212/wnl.0000000000012489
Jaclyn Tencer 1 , Sabrina W Yum 1
Affiliation  

An 18-year-old man with type 1 diabetes presented with acute bilateral arm and leg ballismus and oral-buccal dyskinesia. Glucose was 394 and HgbA1c >14. Imaging revealed T1 hyperintensity and susceptibility effect within the basal ganglia (Figure). Symptoms resolved over 48 hours with glucose control. A diagnosis of diabetic striatopathy was made. Diabetic striatopathy, also called hyperglycemic hemiballism/hemichorea, is most often described in older individuals with type 2 diabetes. Clinical symptoms often resolve with glycemic control; however, many patients require pharmacologic treatments. Deep brain stimulation may be beneficial in cases with disabling involuntary movements. Hyperglycemia-induced vasculopathy may contribute to microhemorrhages on imaging.1,2



中文翻译:

NeuroImage 教学:1 型 1 型糖尿病患者的 18 岁男性基底节 T1 高信号和 SWI 信号糖尿病纹状体病

一名患有 1 型糖尿病的 18 岁男性出现急性双侧手臂和腿部弹道痉挛和口腔-颊部运动障碍。葡萄糖为 394,HgbA1c >14。成像显示基底节内的 T1 高信号和易感性效应(图)。通过血糖控制,症状在 48 小时内消退。诊断为糖尿病性纹状体病。糖尿病性纹状体病,也称为高血糖偏头痛/偏舞蹈症,最常见于患有 2 型糖尿病的老年人。临床症状通常随着血糖控制而消退;然而,许多患者需要药物治疗。在禁用不自主运动的情况下,深部脑刺激可能是有益的。高血糖引起的血管病变可能导致成像上的微出血。1,2

更新日期:2021-11-23
down
wechat
bug