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Pearls & Oy-sters: POEMS Syndrome: An Eloquent Acronym for a Rare Disease You Don't Want to Miss
Neurology ( IF 7.7 ) Pub Date : 2021-10-26 , DOI: 10.1212/wnl.0000000000012325 Abigail Bossart 1 , Brian McClune 1 , Kelsey Barrell 1 , Judith Warner 1 , Jennifer Juhl Majersik 1
中文翻译:
珍珠和牡蛎:POEMS 综合征:一种您不想错过的罕见疾病的雄辩首字母缩略词
更新日期:2021-10-26
Neurology ( IF 7.7 ) Pub Date : 2021-10-26 , DOI: 10.1212/wnl.0000000000012325 Abigail Bossart 1 , Brian McClune 1 , Kelsey Barrell 1 , Judith Warner 1 , Jennifer Juhl Majersik 1
Affiliation
POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal protein, and skin changes) must be considered for patients with chronic inflammatory demyelinating polyradiculopathy (CIDP) not responding to corticosteroids, IV immunoglobulin (IVIg) therapy, or plasmapheresis.
中文翻译:
珍珠和牡蛎:POEMS 综合征:一种您不想错过的罕见疾病的雄辩首字母缩略词
对于皮质类固醇、静脉注射免疫球蛋白 (IVIg) 治疗或血浆置换术无反应的慢性炎症性脱髓鞘性多发性神经根病 (CIDP) 患者,必须考虑 POEMS 综合征(多发性神经病、器官肿大、内分泌病、单克隆蛋白和皮肤改变)。