An early repolarization (ER) pattern or J waves are considered to be a benign finding observed in the healthy population, however, it has been pointed out that the ER pattern seen in the inferolateral leads could be an independent risk factor for fatal arrhythmias. We present a pediatric case in which early repolarization syndrome (ERS) was suspected due to the presence of ER or J waves in the inferior leads, which eventually disappeared after the administration of pilsicainide. During the follow-up period, several fatal ventricular arrhythmias were recorded after implantation of a subcutaneous implantable cardiac defibrillator (S-ICD). This report describes the efficacy of S-ICDs in a child with an ER pattern after aborted sudden cardiac death.

早期复极 (ER) 模式或 J 波被认为是在健康人群中观察到的良性发现，然而，有人指出在下外侧导联中看到的 ER 模式可能是致命性心律失常的独立危险因素。我们介绍了一个儿科病例，其中由于下导联中存在 ER 或 J 波而怀疑早期复极综合征 (ERS)，在使用匹西卡尼后最终消失。在随访期间，皮下植入式心脏除颤器 (S-ICD) 植入后记录了数起致命的室性心律失常。本报告描述了 S-ICD 对流产性心源性猝死后 ER 型儿童的疗效。