Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare, aggressive hematologic malignancy that can present with multiorgan involvement including the skin. While this entity accounts for 0.1% of all cutaneous lymphomas in adults, fewer than 90 pediatric cases have been described in the literature. We present three cases of pediatric BPDCN, highlighting the variable cutaneous and clinical presentation.

中文翻译：

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具有皮肤表现的母细胞性浆细胞样树突状细胞肿瘤：儿童病例系列

母细胞性浆细胞样树突细胞肿瘤 (BPDCN) 是一种罕见的侵袭性血液系统恶性肿瘤，可表现为包括皮肤在内的多器官受累。虽然该实体占成人所有皮肤淋巴瘤的 0.1%，但文献中描述的儿科病例不到 90 例。我们介绍了三个小儿 BPDCN 病例，重点介绍了可变的皮肤和临床表现。