ABSTRACT

Aim: To verify and compare trunk control and upper limb functionality (ULs) in walking and non-walking DMD individuals, with that of individuals without dystrophinopathies.Method: Cross-sectional study, with children without dystrophinopathy (healthy control group) and in walking and non-walking DMD children evaluated by the following scales: Segmental Control Evaluation Trunk (SATCo); Performance of Upper Limb (PUL) and Jebsen-Taylor Test (JTT).Results: There was a difference between the groups in trunk control and ULs function by the PUL scale, but there was no difference between walking and the reference group in all JTT subtests; The JTT writing subtest was not different between groups. There was a strong correlation between PUL and SATCo, both had a strong correlation with disease staging and a weak correlation with JTT.Conclusions: There is relevance to the evaluation of trunk control and ULs function of walking and non-walking DMD.

摘要

目的：验证和比较行走和非行走 DMD 个体的躯干控制和上肢功能 (UL)，与没有肌营养不良症的个体的躯干控制和上肢功能 (UL)。方法：横断面研究，对没有肌营养不良症的儿童（健康对照组）以及步行和非步行 DMD 儿童进行以下量表评估：节段控制评估树干 (SATCo)；上肢 (PUL) 和 Jebsen-Taylor 测试 (JTT) 的性能。结果：根据 PUL 量表，在躯干控制和 ULs 功能方面，各组之间存在差异，但在所有 JTT 子测试中，步行和参考组之间没有差异；JTT 写作分测验在各组之间没有差异。PUL 和SATCo 之间有很强的相关性，两者都与疾病分期有很强的相关性，而与JTT 的相关性很弱。结论：与步行和非步行 DMD 的躯干控制和 ULs 功能的评估相关。