Capillary hemangiomas (CHs) of the central nervous system represent a rare diagnosed pathology. CHs are benign vascular tumors whose most common manifestations are dermal and mucous and mainly occur during childhood or adolescence, while the involvement of the central nervous system can occur in a wider age range. We conducted a PubMed research on literature published until March 2020. We only enrolled cases with histological documented presence of intracranial CH. For every case collected, we analyzed age, sex, localization, neuroimaging studies performed, the presence of extracranial CHs, symptoms, neurological deficits, extent of surgical resection (biopsy, partial or gross total), adjunct treatment received (radiotherapy, chemotherapy, Trans-Arterial Embolization TAE), and outcome. Up to March 2020, the literature review identified 52 cases to which we added the case of our personal experience. The mean age was 26 with slightly female prevalence (28 F, 25 M). The most common presenting symptom was headache (21 cases, 40%). The surgical treatment consisted of biopsy in 7 cases (13%), partial resection in 10 cases (19%), gross total resection in 31 cases (58.5%), biopsy followed by total resection in 2 cases (3%), and partial resection followed by total resection in 1 case (1.5%), and the diagnosis was obtained from an autopsy sample in 1 case (1.5%). For symptomatic lesions, surgery is a valid option to obtain histological characterization, neurological improvement, and where possible a total resection. Stereotactic radiotherapy can be used if the lesion is not surgically approachable or as an adjuvant treatment in case of partial resection, having shown good results in terms of long-term disease control.

中枢神经系统的毛细血管瘤 (CHs) 是一种罕见的诊断病理。CH是良性血管肿瘤，最常见的表现是皮肤和粘液，主要发生在儿童期或青春期，而中枢神经系统受累的年龄范围更广。我们对 2020 年 3 月之前发表的文献进行了 PubMed 研究。我们只招募了组织学记录存在颅内 CH 的病例。对于收集的每个病例，我们分析了年龄、性别、定位、进行的神经影像学研究、颅外 CHs 的存在、症状、神经功能缺损、手术切除的范围（活检、部分或全部）、接受的辅助治疗（放疗、化疗、跨-动脉栓塞 TAE）和结果。截至 2020 年 3 月，文献综述确定了 52 个案例，我们在其中添加了我们的个人经历案例。平均年龄为 26 岁，女性患病率较低（28 F，25 M）。最常见的症状是头痛（21 例，40%）。手术治疗包括活检7例（13%），部分切除10例（19%），大体全切除31例（58.5%），活检后全切除2例（3%），部分切除。 1 例（1.5%）切除后全切除，1 例（1.5%）从尸检样本中获得诊断。对于有症状的病变，手术是获得组织学特征、神经系统改善和可能的全切除术的有效选择。如果病变无法通过手术接近或作为部分切除的辅助治疗，则可以使用立体定向放疗，