Lymphocytic cholangitis is a rare Porto‐hepatic disease with predominant infiltration of lymphocytes and plasma cells in the portal tracts of the liver. X‐linked lymphoproliferative disease is an inborn error of immunity caused by a defect in the signaling lymphocyte‐activation molecule (SLAM)‐associated protein. Lymphocytic cholangitis is reported in feline species, however, reports in humans is scarce. We report the first case of Epstein‐Barr Virus‐related lymphocytic cholangitis in a child with X‐linked lymphoproliferative syndrome.

中文翻译：

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爱泼斯坦巴尔病毒相关的淋巴细胞性胆管炎的儿童与X连锁的淋巴增生性综合征。

淋巴细胞性胆管炎是一种罕见的肝门静脉疾病，主要在肝门静脉中浸润淋巴细胞和浆细胞。X连锁淋巴组织增生性疾病是由信号性淋巴细胞激活分子（SLAM）相关蛋白缺陷引起的免疫力先天性错误。猫科动物中有淋巴细胞性胆管炎的报道，但是人类中的报道却很少。我们报道了第一例与X连锁淋巴组织增生综合征患儿有关的爱泼斯坦-巴尔病毒相关的淋巴细胞性胆管炎。