With improvements in the outcomes for cholestatic liver diseases that present in childhood, increasing numbers of patients will require ongoing care as adults. The recent advances in management options coupled with the fact that each adult physician will have a limited number of patients with these conditions means there is a need for those in adult services to develop expertise in these conditions that were historically the domain of paediatrics. This review provides an overview of the most common paediatric cholestatic liver diseases and outlines the clinical manifestations and potential complications, and identifies key management issues unique to each condition for effective ongoing care of these patients.

中文翻译：

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成人胃肠病学家的小儿胆汁淤积性肝病：实用指南

随着儿童期胆汁淤积性肝病预后的改善，越来越多的患者将需要成年后的持续护理。管理方案的最新进展，加上每位成年医生将有数量有限的患有这些疾病的患者这一事实，意味着成人服务人员需要在这些疾病方面发展专业知识，而这些疾病历来是儿科的领域。本综述概述了最常见的小儿胆汁淤积性肝病，概述了临床表现和潜在并发症，并确定了每种疾病特有的关键管理问题，以便对这些患者进行有效的持续护理。