“Hair-thread tourniquet syndrome” (HTTS) describes the condition in which fibers of hair or thread wrap around an appendage (ie, toes, fingers, genital structures, tongue, uvula, and neck), eventually causing ischemia and tissue necrosis. To date, few cases of female genitalia HTTS have been described. We report a case of female genitalia HTTS in a 5-year-old girl and report the state of the art by systematically reviewing all existing evidence about female genital HTTS. A total of 29 studies, describing a total of 34 patients, were identified. The presence of a hair-thread wrapping genitalia should be suspected in prepubertal girls complaining of genital pain associated with vulvar/vaginal swelling, wide-based gait, and voiding symptoms. Genital examination disclosing an extremely tender, swollen, and erythematous lesion on the clitoris or labia minora encircled by a hair confirms the diagnosis. The aim of the management is to remove the hair-thread in the shortest time possible, with the use of forceps, scissors, or scalpels, and this is often performed under sedation/anesthesia because of the patient's pain reaction. When the hair-thread is difficult to find or when the lesion is necrotic, excision of the lesion itself can be the only option. Complications include partial or total amputation because of tissue necrosis and recurrence.

“头发线止血带综合征”（HTTS）描述了一种状况，其中头发或线的纤维缠绕在附件（即脚趾，手指，生殖器结构，舌头，悬雍垂和脖子）周围，最终导致局部缺血和组织坏死。迄今为止，很少有女性生殖器HTTS病例的描述。我们报告了一个5岁女孩的女性生殖器HTTS病例，并通过系统地审查了有关女性生殖器HTTS的所有现有证据来报告了最新技术水平。总共鉴定了29项研究，描述了总共34例患者。在青春期前的女孩中，如果抱怨与外阴/阴道肿胀，步态宽阔和排尿症状有关的生殖器疼痛，则应怀疑存在缠发丝的生殖器。生殖器检查发现极度柔软，肿胀，毛发包围的阴蒂或小阴唇上的红斑病变可确诊。管理的目的是使用镊子，剪刀或手术刀在最短的时间内去除毛发，由于患者的疼痛反应，通常在镇静/麻醉下进行。当难以找到发丝或病变坏死时，切除病变本身可能是唯一的选择。并发症包括由于组织坏死和复发而导致部分或全部截肢。当难以找到发丝或病变坏死时，切除病变本身可能是唯一的选择。并发症包括由于组织坏死和复发而导致部分或全部截肢。当难以找到发丝或病变坏死时，切除病变本身可能是唯一的选择。并发症包括由于组织坏死和复发而导致部分或全部截肢。