Purpose

Persistent left superior vena cava (PLSVC) with absent right superior vena cava (ARSVC) is rare. We evaluated CT and clinical findings of adults with ARSVC.

Materials and methods

Our study included 11 adults with ARSVC (mean age, 63 ± 17 years). We evaluated CT findings of the azygos vein system and coronary sinus (CS) using thin slice data of > 64 MDCT. Arrhythmia and congenial heart disease were assessed. We compared the CS diameters between the ARSVC group and the control group of 120 adults with normal vena cava (mean age, 60 ± 4 years).

Results

Adults with ARSVC had no azygos vein arch and the hemiazygos vein continued to PLSVCs via the superior intercostal vein. Eight adults had arrhythmia including conduction disturbance and one arrhythmia was associated with atrial septal defect. All adults with ARSVC had dilated CS larger than 11 mm. The mean diameter of the CS in the ARSVC group was 18.4 mm, and that of the control group was 6.8 mm. CS diameter in the ARSVC group was larger than that in the control group (p < 0.001).

Conclusion

Adults with ARSVC had dilated CS and no azygos vein arch. Four adults had conduction disturbance.

中文翻译：

---

成人持续左上腔静脉伴右上腔静脉缺失：CT和临床表现。

目的

很少有持续的左上腔静脉（PLSVC）和不存在的右上腔静脉（ARSVC）。我们评估了成人ARSVC的CT和临床表现。

材料和方法

我们的研究包括11名ARSVC成人（平均年龄63±17岁）。我们使用> 64 MDCT的薄片数据评估了奇静脉系统和冠状窦（CS）的CT表现。评估心律不齐和先天性心脏病。我们比较了ARSVC组和对照组的120名正常腔静脉成年人（平均年龄，60±4岁）的CS直径。

结果

患有ARSVC的成人没有奇合子静脉弓，并且半合子静脉通过肋间上静脉继续进入PLSVCs。8名成年人发生心律失常，包括传导障碍，其中1名心律失常与房间隔缺损相关。所有患有ARSVC的成人均已将CS扩张大于11毫米。ARSVC组中CS的平均直径为18.4 mm，对照组为6.8 mm。ARSVC组的CS直径大于对照组（p  <0.001）。

结论

患有ARSVC的成人扩张了CS，无奇静脉弓。四名成年人有传导障碍。