Background

The cystic spinal dysraphism of the cervical and upper thoracic region (CDCT) accounts for only 3.9 to 8% of spina bifida cystica lesions. The presence of external cerebrospinal fluid (CSF) leakage is infrequent and very few authors have reported about surgical complications.

Case report

We present the case of a new born diagnosed of CDCT C1-C3 with a stalk of fibrovascular tissue, CSF leakage, hydrocephalus, and type Chiari II malformation, discuss about the chosen surgical technique and the associated complications, and make a review of the literature focusing on the main aspects of CDCT.

Conclusions

The CDCT with a stalk of neuroglial and/or fibrovascular tissue originates from the dorsal surface of the spinal cord and penetrates into a cervical cystic sac. The presence of CSF leakage, hydrocephalus, and/or type Chiari II malformation can influence to decide the most appropriate surgical technique.

中文翻译：

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伴有脑脊液漏的颈脊髓脊膜膨出：基于病例的回顾。

背景

颈部和上胸区（CDCT）的囊性脊柱裂隙症仅占囊性脊柱裂病变的 3.9% 至 8%。外部脑脊液 (CSF) 渗漏的存在并不常见，很少有作者报告过手术并发症。

案例报告

我们介绍一例诊断为CDCT C1-C3的新生儿，伴有纤维血管组织柄、脑脊液漏、脑积水和Chiari II型畸形，讨论了所选择的手术技术和相关并发症，并对文献进行了回顾重点关注CDCT的主要方面。

结论

具有神经胶质和/或纤维血管组织茎的 CDCT 起源于脊髓的背侧表面并穿透到颈部囊性囊中。脑脊液漏、脑积水和/或 Chiari II 型畸形的存在会影响决定最合适的手术技术。