The Academy of Nutrition and Dietetics Evidence Analysis Center conducted a systematic review of the literature to develop an evidence-based practice guideline for primary nutrition issues in cystic fibrosis (CF). This guideline is designed to complement and build upon existing evidence-based CF nutrition guidelines. The objective of this guideline was to provide recommendations for registered dietitian nutritionists in the United States delivering medical nutrition therapy to individuals with CF and their families that fill gaps in current evidence-based guidelines on topics that are crucial in order to improve health and prevent disease progression. This guideline provides 28 nutrition recommendations to guide medical nutrition therapy, including nutrition screening, nutrition assessment, and dietary intake. For topics outside the scope of this guideline, practitioners are referred to external, evidence-based recommendations. The CF landscape is evolving rapidly with breakthroughs in cystic fibrosis transmembrane regulator modulators changing CF at a cellular level. Medical nutrition therapy for individuals with CF from infancy through advanced age requires novel and individualized approaches. The Academy Evidence Analysis Library CF guidelines provide a framework for expanding upon current knowledge to determine effective nutrition strategies for individuals with CF through long and healthy futures.

营养与饮食学会证据分析中心对文献进行了系统回顾，为囊性纤维化（CF）的初级营养问题制定了循证实践指南。本指南旨在补充和建立现有循证 CF 营养指南。该指南的目的是为美国注册营养师向 CF 患者及其家人提供医学营养治疗提供建议，填补当前循证指南中关于改善健康和预防疾病至关重要的主题的空白进展。该指南提供了28条营养建议来指导医学营养治疗，包括营养筛查、营养评估和膳食摄入。对于本指南范围之外的主题，从业者会参考外部基于证据的建议。随着囊性纤维化跨膜调节剂在细胞水平上改变 CF 的突破，CF 领域正在迅速发展。对从婴儿期到高龄的 CF 患者进行医学营养治疗需要新颖和个体化的方法。学院证据分析图书馆 CF 指南提供了一个框架，用于扩展当前知识，以确定 CF 患者长期健康未来的有效营养策略。