Background Papillary tumor of the pineal region is an unusual, recently described entity with potential for misinterpretation as either an ependymoma or choroid plexus papilloma. With few reported cases, there is little data regarding the biologic behavior, natural course and optimal treatment for these patients. Further accumulation of reports will assist with defining this entity and may provide further insight into management of such patients. Case presentation This patient was a 24-year-old male with new onset seizures and a decreased level of consciousness. MRI scan showed a large heterogeneously enhancing solid-cystic mass in the pineal region extending to the third ventricle. Discussion Papillary tumor of the pineal region is a neuroepithelial tumor with distinct morphological and immunohistochemical features that can be utilized to help differentiate it from other primary and metastatic tumors occurring within this region. Although there is currently no clear consensus, the potential for disease progression and CSF dissemination supports early aggressive therapy in these patients.

中文翻译：

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松果体区乳头状肿瘤1例报告

背景松果体区的乳头状瘤是一种不寻常的、最近描述的实体，可能被误解为室管膜瘤或脉络丛乳头状瘤。由于报告的病例很少，关于这些患者的生物学行为、自然病程和最佳治疗的数据很少。报告的进一步积累将有助于定义该实体，并可能提供对此类患者管理的进一步了解。病例介绍 该患者是一名 24 岁男性，新发癫痫发作，意识水平下降。MRI 扫描显示松果体区有一个大的不均匀增强的实性囊性肿块，延伸至第三脑室。讨论 松果体区乳头状瘤是一种神经上皮肿瘤，具有独特的形态学和免疫组织化学特征，可用于帮助区分该区域内发生的其他原发性和转移性肿瘤。虽然目前没有明确的共识，但疾病进展和脑脊液传播的可能性支持对这些患者进行早期积极治疗。