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Rare non-Hodgkin lymphoma of childhood and adolescence: A consensus diagnostic and therapeutic approach to pediatric-type follicular lymphoma, marginal zone lymphoma, and nonanaplastic peripheral T-cell lymphoma.
Pediatric Blood & Cancer ( IF 2.4 ) Pub Date : 2020-05-26 , DOI: 10.1002/pbc.28416
Andishe Attarbaschi 1 , Oussama Abla 2 , Laura Arias Padilla 3 , Auke Beishuizen 4 , G A Amos Burke 5 , Laurence Brugières 6 , Julie Bruneau 7 , Birgit Burkhardt 3 , Emanuele S G d'Amore 8 , Wolfram Klapper 9 , Udo Kontny 10 , Marta Pillon 11 , Mary Taj 12 , Suzanne D Turner 13, 14 , Anne Uyttebroeck 15 , Wilhelm Woessmann 16 , Karin Mellgren 17
Affiliation  

Pediatric‐type follicular (PTFL), marginal zone (MZL), and peripheral T‐cell lymphoma (PTCL) account each for <2% of childhood non‐Hodgkin lymphoma. We present clinical and histopathological features of PTFL, MZL, and few subtypes of PTCL and provide treatment recommendations. For localized PTFL and MZL, watchful waiting after complete resection is the therapy of choice. For PTCL, therapy is subtype‐dependent and ranges from a block‐like anaplastic large cell lymphoma (ALCL)‐derived and, alternatively, leukemia‐derived therapy in PTCL not otherwise specified and subcutaneous panniculitis‐like T‐cell lymphoma to a block‐like mature B‐NHL‐derived or, preferentially, ALCL‐derived treatment followed by hematopoietic stem cell transplantation in first remission in hepatosplenic and angioimmunoblastic T‐cell lymphoma.

中文翻译:

少见的少儿非霍奇金淋巴瘤:儿童型滤泡性淋巴瘤,边缘区淋巴瘤和非变性周围性T细胞淋巴瘤的共识性诊断和治疗方法。

儿童型滤泡性(PTFL),边缘区(MZL)和外周T细胞淋巴瘤(PTCL)分别占儿童非霍奇金淋巴瘤的<2%。我们介绍了PTFL,MZL和PTCL的亚型的临床和组织病理学特征,并提供了治疗建议。对于局灶性PTFL和MZL,完全切除后的观察等待是首选治疗方法。对于PTCL,治疗依赖于亚型,范围从块状间变性大细胞淋巴瘤(ALCL)衍生,或者另选未指定PTCL中的白血病源性治疗,皮下脂膜炎样T细胞淋巴瘤至块状。像是成熟的B‐NHL衍生或优先采用ALCL衍生的治疗,然后在肝脾和血管免疫母细胞T细胞淋巴瘤的首次缓解中进行造血干细胞移植。
更新日期:2020-06-23
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