OBJECTIVES The objective of this study was to confirm the validity of a short form of gross motor function measure for Fukuyama congenital muscular dystrophy (GMFM for FCMD). METHODS This study is a case series and was conducted at the Tokyo Women's Medical University. Fifteen patients with FCMD were assessed using both the GMFM for FCMD with 68 items, which was created as a motor function measure for patients with FCMD on the basis of Rasch analysis, and the original GMFM with 88 items. The correlation between the GMFM for FCMD and the Ueda classification was assessed. Time required for each assessment was also evaluated. RESULTS We found significant correlation between the GMFM for FCMD and the Ueda classification (r = 0.935); furthermore, the mean assessment time tended to decrease when using the GMFM for FCMD. CONCLUSIONS GMFM for FCMD may be an appropriate motor function scale for patients with FCMD and might help decrease the assessment time.

中文翻译：

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福山先天性肌营养不良症粗大运动功能测量的简短形式

目的 本研究的目的是确认福山先天性肌营养不良症粗大运动功能测量的简短形式（FCMD 的 GMFM）的有效性。方法 本研究是一个病例系列，在东京女子医科大学进行。15 名 FCMD 患者使用 68 个项目的 FCMD GMFM 进行评估，该 GMFM 是在 Rasch 分析的基础上作为 FCMD 患者的运动功能测量而创建的，以及原始 GMFM 与 88 个项目。评估了 FCMD 的 GMFM 与 Ueda 分类之间的相关性。还评估了每次评估所需的时间。结果 我们发现 FCMD 的 GMFM 与 Ueda 分类之间存在显着相关性 (r = 0.935)；此外，当将 GMFM 用于 FCMD 时，平均评估时间趋于减少。