Hepatic angiosarcoma is a rare malignant tumor featured by highly aggressive behavior and poor prognosis. There are few reports about diffused hepatic angiosarcoma with Kasabach-Merritt syndrome till now. A male patient with the chief complain of hepatic space-occupying lesion accompanied by disturbance of consciousness and jaundice. Hyperbilirubinemia, anemia, thrombocytopenia, prolonged prothrombin time, hypofibrinogenemia, decreased prothrombin activity, and increased fibrinogen degradation product and D-dimer were confirmed by blood analysis; multiple focal hypodense lesions in liver was detected by abdominal computed tomography. Liver failure and Kasabach-Merritt syndrome induced by hepatic hemangioma was diagnosed before operation and liver transplantation was performed. Hepatic angiosarcoma was finally proven by postoperative pathology. This patient died of tumor metastasis 2 months after operation. Hepatic angiosarcoma which can generate Kasabach-Merritt syndrome and even liver failure has an extremely poor prognosis; liver transplantation option should not be considered in hepatic angiosarcoma regardless of the reason.

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扩散性肝血管肉瘤合并卡萨巴赫-梅里特综合征的病例报告及文献复习

肝血管肉瘤是一种罕见的恶性肿瘤，具有高度侵袭性和预后不良的特点。到目前为止，关于卡萨巴-梅里特综合征的弥漫性肝血管肉瘤的报道很少。一名患有主要疾病的男性患者主诉肝脏占位性病变，并伴有意识和黄疸的困扰。血液分析证实高胆红素血症，贫血，血小板减少，凝血酶原时间延长，血纤维蛋白原减少，凝血酶原活性降低，纤维蛋白原降解产物和D-二聚体增加。通过腹部计算机断层扫描检测到肝脏中有多个局灶性低密度病变。在手术和进行肝移植之前，应诊断出由肝血管瘤引起的肝衰竭和卡萨巴赫-梅里特综合征。肝血管肉瘤最终经术后病理证实。该患者术后2个月死于肿瘤转移。可能产生卡萨巴赫-梅里特综合征甚至肝衰竭的肝血管肉瘤的预后极差；无论原因如何，均不应考虑在肝血管肉瘤中选择肝移植方案。