Neurofibromatosis type 1 (NF1), neurofibromatosis type 2 (NF2), and schwannomatosis (SWN) are three clinically distinct tumor predisposition syndromes with a shared tendency to develop peripheral and central nervous system neoplasms. Disease expression and complications of NF1, NF2, and SWN are highly variable, necessitating a multidisciplinary approach to care in order to optimize outcomes. This review will discuss the imaging appearance of NF1, NF2, and SWN and highlight the important role that imaging plays in informing management decisions in people with tumors associated with these syndromes. Recent technological advances, including the role of both whole-body and localized imaging strategies, routine anatomic and advanced magnetic resonance (MR) imaging sequences such as diffusion-weighted imaging (DWI) with quantitative apparent diffusion coefficient (ADC) mapping, and metabolic imaging techniques (MR spectroscopy and positron emission testing) are discussed in the context of the diagnosis and management of people with NF1, NF2, and SWN based on the most up-to-date clinical imaging studies.

中文翻译：

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1型神经纤维瘤病，2型神经纤维瘤病和神经鞘瘤病的影像学现状和建议

1型神经纤维瘤病（NF1），2型神经纤维瘤病（NF2）和神经鞘瘤病（SWN）是三种临床上不同的肿瘤易感综合症，共有发展周围和中枢神经系统肿瘤的趋势。疾病的表达和NF1，NF2和SWN的并发症是高度可变的，因此有必要采用多学科的护理方法以优化结果。这篇综述将讨论NF1，NF2和SWN的影像学表现，并强调影像学在告知患有这些综合征的肿瘤患者的治疗决策中所起的重要作用。最近的技术进步，包括全身和局部成像策略的作用，