We describe a rare case of intracranial malignant triton tumor (MTT) arising in the middle cranial fossa in a 74-year-old female patient who had previously been exposed to radiation in the Chernobyl disaster. The patient underwent a surgical subtotal removal of the mass and radiation therapy, but the progression-free survival was only 2.5 months and death occurred four months after the onset of symptoms. MTTs are rare aggressive tumors arising from the nerve sheath showing rhabdomyosarcomatous differentiation and associated with a poor prognosis. The intracranial location is very rare, and only 10 cases, including the present report, have been described so far. Among intracranial MTTs, the cerebellopontine angle is the most common location. Neurofibromatosis type 1 (NF-1) and radiation exposure are risk factors as for MTTs located in other sites. The gold standard therapy is surgical excision followed by radiation therapy, but the prognosis is usually very poor.

中文翻译：

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颅中部恶性颅内发生颅内恶性Triton肿瘤的罕见病例：1例报道并文献复习。

我们描述了一个罕见的颅内恶性Triton肿瘤（MTT）病例，该病例发生在一名74岁的女性患者的颅中窝，该患者先前曾在切尔诺贝利灾难中遭受过辐射。病人接受了手术的小计切除肿块和放射疗法，但无进展生存期仅为2.5个月，死亡发生在症状发作后的四个月。MTTs是罕见的侵袭性肿瘤，由神经鞘引起，表现为横纹肌肉瘤分化，预后不良。颅内位置非常少见，迄今为止仅描述了10例病例，包括本报告。在颅内MTT中，小脑桥脑角是最常见的位置。与其他部位的MTT一样，1型神经纤维瘤病（NF-1）和放射线暴露也是危险因素。