Atypical teratoid/rhabdoid tumors (AT/RT) are highly aggressive malignant primitive neoplasms that commonly occur in children younger than 2 years of age. The prognosis is generally dismal with a median survival time of <1 year. The majority of AT/RT occur in the posterior fossa and less frequently the supratentorium. Primary pediatric spinal AT/RT are exceedingly rare and only 15 cases have been reported to date. Here we report a very unusual case of primary spinal AT/RT extensively involving the spinal cord from T11 down to the cauda equina. In this patient, the tumor was highly aggressive and resulted in extensive dissemination into the nerve roots and paraspinal soft tissue rapidly resulting in the patient's death 1 month after diagnosis. to the best of our knowledge, this degree of involvement of the spine by a primary AT/RT has not been described before.

中文翻译：

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儿童马尾非典型畸胎瘤横纹肌瘤

非典型畸胎瘤/横纹肌样瘤 (AT/RT) 是高度侵袭性的恶性原始肿瘤，常见于 2 岁以下的儿童。预后通常很差，中位生存时间<1年。大多数 AT/RT 发生在后颅窝，较少发生在幕上。原发性小儿脊柱 AT/RT 极为罕见，迄今为止仅报告了 15 例。在这里，我们报告了一个非常不寻常的原发性脊髓 AT/RT 病例，广泛涉及从 T11 到马尾的脊髓。在该患者中，肿瘤具有高度侵袭性，导致广泛扩散到神经根和椎旁软组织，导致患者在诊断后 1 个月死亡。据我们所知，