This Review provides an updated approach to the diagnosis of idiopathic pulmonary fibrosis (IPF), based on a systematic search of the medical literature and the expert opinion of members of the Fleischner Society. A checklist is provided for the clinical evaluation of patients with suspected usual interstitial pneumonia (UIP). The role of CT is expanded to permit diagnosis of IPF without surgical lung biopsy in select cases when CT shows a probable UIP pattern. Additional investigations, including surgical lung biopsy, should be considered in patients with either clinical or CT findings that are indeterminate for IPF. A multidisciplinary approach is particularly important when deciding to perform additional diagnostic assessments, integrating biopsy results with clinical and CT features, and establishing a working diagnosis of IPF if lung tissue is not available. A working diagnosis of IPF should be reviewed at regular intervals since the diagnosis might change. Criteria are presented to establish confident and working diagnoses of IPF.

中文翻译：

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特发性肺纤维化的诊断标准：Fleischner Society白皮书。

这篇综述基于对医学文献的系统搜索和弗莱什纳学会成员的专家意见，为诊断特发性肺纤维化（IPF）提供了一种更新的方法。提供了一份清单，用于怀疑可疑的普通间质性肺炎（UIP）患者的临床评估。当CT显示可能的UIP模式时，在某些情况下，CT的作用得以扩展，无需手术肺活检即可诊断IPF。对于IPF不确定的临床或CT表现患者，应考虑进行其他检查，包括手术肺活检。在决定进行其他诊断评估，将活检结果与临床和CT特征结合在一起时，多学科方法特别重要，如果没有肺组织，则可以建立IPF的工作诊断。应定期检查IPF的有效诊断，因为诊断可能会改变。提出了建立对IPF的自信和有效诊断的标准。