When classifying pulmonary hypertension, the terms precapillary and post-capillary are used to describe the most likely origin of pulmonary vascular disease. The term idiopathic pulmonary arterial hypertension describes a distinct type of pre-capillary pulmonary hypertension, characterised by progressive pulmonary vascular remodelling in the absence of other diseases explaining the presence of pulmonary hypertension.^1,2 In historical cohorts, idiopathic pulmonary arterial hypertension was diagnosed predominantly in young women.

中文翻译：

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是否有消失的肺毛细血管综合症？

在对肺动脉高压进行分类时，术语毛细血管前和毛细血管后被用来描述肺血管疾病的最可能起源。术语特发性肺动脉高压描述了一种不同类型的毛细血管前性肺动脉高压，其特征是在没有其他疾病的情况下进行性肺血管重构，从而解释了肺动脉高压的存在。^1,2在历史人群中，年轻女性主要被诊断为特发性肺动脉高压。