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Intracranial kaposiform hemangioendothelioma presenting as epistaxis: a rare case report with review of literature

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Abstract

Introduction

Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor of intermediate malignancy with tendency for local invasion and recurrence. The tumor almost exclusively occurs in children, especially in infants. Intracranial KHE are extremely rare with only two cases reported in the literature.

Report

We report the clinical and pathological features of this rare tumor arising from basitemporal region in a 21-month child. Our case did not present with Kasabach-Merritt phenomenon. Histopathological examination confirmed the diagnosis of KHE.

Conclusion

KHE should be considered in the differential diagnosis of intracranial extra-axial neoplasm in children, and histopathological examination plays an important role in distinguishing KHE from its morphologic mimics. It is essential to diagnose KHE due to its locally aggressive nature.

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Authors and Affiliations

  1. Departments of Neuropathology, National Institute of Mental Health and Neurosciences, Bangalore, India

    Soutrik Das & Shilpa Rao

  2. Departments of Neurosurgery, National Institute of Mental Health and Neurosciences, Bangalore, India

    Harsh Deora & Sandeep Kandregula

  3. Department of Pathology, Kidwai Memorial Institute of Oncology, Bangalore, India

    Suma Mysore Narayana

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  1. Soutrik Das
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  2. Harsh Deora
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  3. Shilpa Rao
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  4. Sandeep Kandregula
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  5. Suma Mysore Narayana
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Correspondence to Shilpa Rao.

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Das, S., Deora, H., Rao, S. et al. Intracranial kaposiform hemangioendothelioma presenting as epistaxis: a rare case report with review of literature. Childs Nerv Syst 37, 2057–2062 (2021). https://doi.org/10.1007/s00381-020-04905-y

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  • DOI: https://doi.org/10.1007/s00381-020-04905-y

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