Abstract
Introduction
Sphenoid dysplasia is a distinctive marker of neurofibromatosis 1. It is a malformation of the sphenoid bone characterized by an enlargement of the superior orbital fissure, through which the intracranial content herniates, leading to a facial disfigurement and exophthalmos and to a potential visual deterioration. Surgical treatment has the aim of separating the intracranial from the intraorbital space.
Methods and results
We present a new technique for the repair of sphenoid dysplasia, based on the preoperative planning on a 3D print of the skull base.
Conclusions
The use of a 3D skull base model allows an effective surgical planning and a precise modelling of the titanium mesh, which is implanted to separate the intracranial from the intraorbital space.
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Data availability
Data sharing is not applicable to this article as no datasets were generated or analysed during the current study.
References
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All authors contributed equally to this work. PS designed the research. MV analysed the data. PS collected the data. PS, MV, and AB wrote the paper. All authors read and approved the final manuscript.
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Informed consent (approved by the Ethical Committee of the University Medical Centre Ljubljana) has been obtained from the parents of the patients included in the study.
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Authors declare no conflict of interests.
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Spazzapan, P., Verdenik, M. & Eberlinc, A. Preoperative planning with a 3D model and repair of sphenoid dysplasia: a technical note. Childs Nerv Syst 36, 2079–2082 (2020). https://doi.org/10.1007/s00381-020-04759-4
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DOI: https://doi.org/10.1007/s00381-020-04759-4