Abstract
The hyper IgM syndromes are a group of rare primary immunodeficiency disorders. Currently 6 classes of HIGM are described. X-linked HIGM is also called the type 1 HIGM is the commonest variant in which children present in early infancy with features of combined immunodeficiency. Tuberculosis is a very rare presentation as a presenting symptom in HIGM. Here, we describe a child with XHIGM with recurrent tuberculosis.
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Krishnan, V.P., Taur, P., Pandrowala, A. et al. X-Linked Hyper IgM Syndrome Presenting with Recurrent Tuberculosis—a Case Report. J Clin Immunol 40, 531–533 (2020). https://doi.org/10.1007/s10875-020-00747-0
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DOI: https://doi.org/10.1007/s10875-020-00747-0