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Anesthetic Management with Propofol in a Patient with Rasmussen's Encephalitis Complicated by Intractable Partial-Onset Epileptic Seizures: A Case Report. Case Rep. Neurol. Pub Date : 2023-10-26 Mai Akazawa,Guoshan Yan,Rina Hirai,Hirotoshi Kitagawa
Introduction Rasmussen's encephalitis (RE) is a progressive and chronic ailment characterized by drug-resistant epileptic seizures. RE is uncommon, and no documented accounts of its anesthetic management exist. Anesthetic management without causing epileptic seizures is important in RE. Here, we present a case of safe anesthetic management in a pediatric patient with RE. Case Presentation A 7-year-old
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Baló Concentric Sclerosis Mimicking Encephalitis with Seizures and Progressive Aphasia in a 26-Year-Old Woman: A Challenging Diagnostic Dilemma. Case Rep. Neurol. Pub Date : 2023-10-06 Nexhmedin Shala,Ilir Tolaj,Fisnik Jashari,Edita Malazogu,Argjend Shala,Gentiant Bajraktari,Ilir Ahmetgjekaj,Shemsedin Dreshaj
Introduction Baló's concentric sclerosis (BCS) is a rare subtype of multiple sclerosis characterized by inflammatory demyelination within the central nervous system. Case Presentation This case report presents a challenging diagnostic scenario involving a 26-year-old woman diagnosed with BCS. Despite treatment, her condition did not ameliorate, and magnetic resonance imaging (MRI) findings remained
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A Rare Case of Cardioembolic Spinal Stroke in a Young Female: Case Report. Case Rep. Neurol. Pub Date : 2023-09-26 Rom Mendel,Irina Tsirkin,Eugene Soikher,Salo Haratz
Spinal cord infarction (SCI) is a rare neurovascular disorder often presented with acute spinal cord syndrome. The diagnosis is generally made clinically, with appropriate neuroimaging to confirm the diagnosis and exclude other causes. We present an unusual case of a 48-year-old woman with no relevant past medical history, admitted with acute paraparesis and a spinal cord infarct on magnetic resonance
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Brait-Fahn-Schwartz Disease: A Unique Co-Occurrence of Parkinson's Disease and Amyotrophic Lateral Sclerosis. Case Rep. Neurol. Pub Date : 2023-09-21 Ayesha Aslam,Eisham Sarmad,Ahmad Nawaz,Ahsan Numan,Azba Ahmad,Muhammad Aarish Hassan
The Parkinson's disease-amyotrophic lateral sclerosis (ALS) complex typically manifests as levodopa-responsive parkinsonism, followed by ALS. It is extremely rare for Parkinson's disease and ALS to coexist without other neurological disorders. Named after the scientists who first described this overlap of two neurodegenerative conditions, it is referred to as Brait-Fahn-Schwartz disease. Given its
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Transcirculation Approach for Matricidal Carotid Cavernous Aneurysm: Not a Good Choice - A Case Report of Unsuccessful Endovascular Treatment of Matricidal Carotid Cavernous Aneurysm. Case Rep. Neurol. Pub Date : 2023-09-04 Norbert Svoboda,Jozef Malik,Frantisek Charvat,David Netuka
Matricidal carotid cavernous aneurysm (CCA) is a rare and dangerous condition. The treatment failure of the endovascular approach like flow diversion, coiling, or stent-coiling is relatively high with considerable morbidity and mortality. The transcirculation approach is an alternative treatment option, but in case of matricidal CCAs, the results are not well documented in the literature. The authors
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Recurrent Acute on Chronic Respiratory Failure in Stiff Person Syndrome. Case Rep. Neurol. Pub Date : 2023-08-22 Bhumika Bheemavarapu,Arkaja Singh,Nived Jayaraj Ranjini,Venkata Sai Abhilash Meda,Dhrumil Patil
Stiff person syndrome (SPS) is an extremely rare disease that presents with episodic painful muscle spasms and progressive muscle rigidity. Recent evidence suggests that SPS can rarely manifest with life-threatening respiratory complications. However, the pathophysiology behind respiratory failure in SPS is still not clearly understood. Here, we explored an extremely rare case of a 36-year-old African-American
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Botulinum Toxin-A for the Treatment of Neuropathic Pain after Decompressive Craniotomy in Stroke: Two Cases. Case Rep. Neurol. Pub Date : 2023-08-22 Yvonne Teuschl,Christian Bancher,Alexandra Dachenhausen,Karl Matz,Michaela M Pinter
Botulinum toxin-A (BoNT-A) is recommended as third-line off-label treatment for the management of neuropathic pain. BoNT-A has been reported as treatment for different neuropathic pain conditions; however, not for neuropathic pain after decompressive craniotomy for stroke. The aim of this retrospective case series is to provide information on safety, the effect, and the application method of BoNT-A
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Prodromal Dementia with Lewy Bodies: A Case Series of the 3 Prodromal Types from Clinical Practice. Case Rep. Neurol. Pub Date : 2023-08-11 Tracy Tholanikunnel,Benjamin Chapin,Melissa Armstrong
Prodromal dementia with Lewy bodies (DLB) refers to a state prior to the onset of dementia with clinical signs or symptoms that may indicate the future development of DLB. Prodromal symptoms can include not only cognitive deficits but also a mix of clinical features including sleep disorders, autonomic dysfunction, and neuro-psychiatric disturbances. While diagnostic criteria for the subtypes of prodromal
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Symmetric Ascending Paralysis Secondary to West Nile Virus. Case Rep. Neurol. Pub Date : 2023-07-13 Alex Ashkin,Nicole Saccone,Jose Valle,Mark Rasnake
West Nile virus (WNV) is classified as a Flavivirus, belonging to a Japanese encephalitis subgroup often transmitted via mosquitoes. The classic presentation of a WNV infection usually displays high fevers, myalgias, and headache which can progress to neck stiffness, stupor, and coma (Case Rep Infect Dis. 2020;2020:6501658). Our case study presented with a rare manifestation of ascending paralysis
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Persistent Hiccups after Subthalamic Nucleus Deep Brain Stimulator Implantation for Parkinson's Disease: Case Report and Literature Review. Case Rep. Neurol. Pub Date : 2023-06-23 Andrew Waack,Michael E Maddens,Nicholas J Maddens,Adam Kuhlman,Michael D Staudt
Hiccups are mediated by a reflex arc that consists of afferent, central, and efferent components. The structures involved in the central component have not been fully elucidated, although several brainstem structures have been implicated, including the subthalamic nucleus (STN). Accordingly, Parkinson's disease (PD), a disease defined by the loss of dopaminergic neurons in the STN, has an interesting
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Encephalitis as a Clinical Manifestation of COVID-19: A Case Series. Case Rep. Neurol. Pub Date : 2023-06-15 Muhammad Hammad Sharif,Madeeha Khaleeque,Asad Ali Khan,Muhammad Hassan Jan,Atif Ahmed,Nida Latif,Abdul Qadir,Muhammad Hanif,Amjid Iqbal
COVID-19 is a novel virus which causes a variety of clinical manifestations in the body, some of which are yet to be discovered. The main aim of our study is to highlight the neurological manifestations of COVID-19 as it is still new to the medical world, and to emphasize the fact that the physicians have to be wary of the possibility that patients affected by COVID-19 can present with encephalitis
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Thirty-Year Follow-Up of Early Onset Amyotrophic Lateral Sclerosis with a Pathogenic Variant in SPTLC1. Case Rep. Neurol. Pub Date : 2023-06-12 Aparna Ajjarapu,Shawna M E Feely,Michael E Shy,Christina Trout,Stephan Zuchner,Steven A Moore,Katherine D Mathews
Dominant mutations in serine palmitoyltransferase long chain base subunit 1 (SPTLC1), a known cause of hereditary sensory autonomic neuropathy type 1 (HSAN1), are a recently identified cause of juvenile amyotrophic lateral sclerosis (JALS) with slow progression. We present a case of SPTLC1-associated JALS followed for 30 years. She was initially evaluated at age 22 years for upper extremity weakness
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Cytotoxic Lesions beyond the Corpus Callosum Following Acute Meningoencephalitis and Mycoplasma Pneumoniae Infection: A Case Report and Literature Review. Case Rep. Neurol. Pub Date : 2023-06-12 Kuan-Hsien Lu,Te-Chang Wu,Poh-Shiow Yeh
Cytotoxic lesions of the corpus callosum (CLOCCs) are secondary lesions associated with a variety of clinical causes. The presence of a small and reversible lesion in the splenium of corpus callosum with restricted diffusion on cranial magnetic resonance imaging is the defining feature. The clinical-radiological manifestations have been documented as mild and reversible. Severer presentations were
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Cerebral Sinus Vein Thrombosis following Sneezing: Case Report. Case Rep. Neurol. Pub Date : 2023-06-12 Helal Nashef,Salo Haratz,Rom Mendel
Cerebral sinus vein thrombosis (CVT) is a relatively rare neurovascular entity, usually associated with acquired or genetic hypercoagulable states, and in many cases it remains idiopathic. Trauma is also associated with CVT among patients with major head or neck trauma, including penetrating injuries. However, CVT associated with acceleration trauma has only been described in few cases so far. We present
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Isoniazid-Induced Psychosis in a Patient with Pulmonary Tuberculosis: A Case Report. Case Rep. Neurol. Pub Date : 2023-06-08 Shreshth Khanna,Suchita Pant,Harsh Khanna
Isoniazid is one of the most important drugs in the management of pulmonary tuberculosis; of all the antituberculous drugs, it is one of the most commonly implicated drugs in drug-induced psychosis. We report a case of isoniazid-induced psychosis in a 31-year-old patient with pulmonary tuberculosis.
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The Inverse Lhermitte Phenomenon Suggests Nitrous Oxide-Induced Myelopathy: Case Report and Review of the Literature. Case Rep. Neurol. Pub Date : 2023-06-08 Sonali Sharma,Michael Benatar,Steven Herskovitz,Volkan Granit
Nitrous oxide-induced myelopathy is a relatively well-known clinical entity. Less well-known, however, is the rare inverse Lhermitte phenomenon, where neck flexion elicits an ascending, rather than descending, electric shock-like sensation. This is a characteristic symptom and sign that may occur in nitrous oxide toxicity. In this article, we present the case of a patient who was admitted to our hospital
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Paraneoplastic Autoimmune Limbic Encephalitis Associated with an Atypical Carcinoid Tumor of the Lung: A Case Report. Case Rep. Neurol. Pub Date : 2023-06-07 Emma Marull Paretas,Claudio De Vito,Sabina Catalano-Chiuve,Maria-Isabel Vargas,Frédéric Assal,Patrice Lalive,Claire Bridel
We report the case of a patient with a history of an atypical lung carcinoid tumor who developed a rapidly progressive memory impairment. The clinical presentation as well as brain MRI, cerebrospinal fluid, and laboratory tests led to the diagnosis of seronegative paraneoplastic autoimmune limbic encephalitis. To the best of our knowledge, this is the first case in literature of such association. This
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Can Growth Hormone Lead to a Faster Recovery from Guillain-Barré Syndrome? Case Report of the First Therapeutic Use in One Patient. Case Rep. Neurol. Pub Date : 2023-06-05 Felix Amereller,Jochen Schopohl,Sylvère Störmann,Katharina Schilbach,Martin Bidlingmaier,Martin Fischer,Peter Rieckmann,Philipp Gulde
Although the prognosis in Guillain-Barré syndrome (GBS) is generally good, protracted and incomplete courses of recovery can be a heavy burden. Animal studies suggest growth hormone (GH) treatment could stimulate myelin repair and thus accelerate functional recovery in acute polyneuropathy. We report on the first use of GH in GBS. Our objective was to monitor safety and tolerability as well as to evaluate
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Unilateral Wing-Beating Tremor in Neuronal Intranuclear Inclusion Disease. Case Rep. Neurol. Pub Date : 2023-06-05 Atsuhiko Sugiyama,Kazuho Kojima,Shigeki Hirano,Jun Sone,Satoshi Kuwabara
Neuronal intranuclear inclusion disease (NIID) is a rare neurodegenerative disease with various neurological manifestations, including tremor. Here, we report a case involving a 68-year-old man with an 8-year history of tremor in his right arm. Subsequently, examination revealed that the patient was suffering from a low-frequency, high-amplitude, and posture-induced proximal arm tremor elicited by
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Contraversive Ocular Tilt Reaction with Contralesional Pseudo-Abducens Palsy in a Patient with Thalamomesencephalic Stroke. Case Rep. Neurol. Pub Date : 2023-06-01 Mohamad Fateh Dabbagh,Lina Okar,Dirk Deleu,Boulenouar Mesraoua
We report a patient presenting with unique neuroophthalmological features of contraversive ocular tilt reaction and concomitant contralesional pseudo-abducens palsy. Magnetic resonance imaging confirmed the presence of an acute infarct in the right thalamomesencephalic region. We discuss the clinical topography of these unique neuroophthalmological findings.
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Hypertrophic Pachymeningitis with Persistent Intrathecal Inflammation Secondary to Neurosarcoidosis Treated with Intraventricular Chemotherapy: A Case Report. Case Rep. Neurol. Pub Date : 2023-06-01 Ana Luísa de Almeida Marcelino,Simon Streit,Marie Alice Homeyer,Hans-Christian Bauknecht,Helena Radbruch,Klemens Ruprecht,Harald Prüss
Hypertrophic pachymeningitis (HP) is a rare immune-mediated disease characterized by thickening of the dura mater with consecutive cranial neuropathy. While HP is usually treated with systemic immunotherapies, response to therapy is variable and may be limited by insufficient drug concentrations in the brain. We report on a 57-year-old patient with HP manifesting with vision and hearing loss who had
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Utilizing Reduced Labeled Proton Clearance to Identify Preclinical Alzheimer Disease with 3D ASL MRI. Case Rep. Neurol. Pub Date : 2023-05-26 Charles R Joseph,Alec Kreilach,Victoria Ashley Reyna,Thomas Ashton Kepler,Brittany Viola Taylor,Jubin Kang,Dallas McCorkle,Nicholas L Rider
Addressing the seminal pathophysiology in Alzheimer disease (AD) is the next logical focus for effective intervention, given the initial disappointing and more recent possibly encouraging results of monoclonal antibody trials. Endothelial cell dysfunction-induced blood-brain barrier leak with associated prolonged capillary mean transit time (cMTT) and glymphatic outflow dysfunction is the most proximal
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Intracranial Stenosis Treated with Stenting in Patients with Suspected Cerebral Vasculitis: Two Case Reports. Case Rep. Neurol. Pub Date : 2023-05-15 Gabriele Vandelli,Laura Giacobazzi,Ludovico Ciolli,Maria Luisa Dell'Acqua,Laura Vandelli,Livio Picchetto,Francesca Rosafio,Giuseppe Maria Borzì,Riccardo Ricceri,Stefano Meletti,Stefano Vallone,Carlo Salvarani,Marco Sebastiani,Federico Sacchetti,Luca Verganti,Stefano Merolla,Gabriele Zelent,Guido Bigliardi
Central nervous system vasculitis (CNSV) is an uncommon and poorly understood form of vasculitis. Early recognition is important because medical treatment might improve the outcome. However, randomized clinical trials on CNSV treatment do not exist. Endovascular treatment has been reported in few cases, but no data exist for intracranial stenting. We report 2 cases of patients with suspected CNSV and
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Improved Osteoarthritis during Erenumab Treatment for Migraine: A Case Report. Case Rep. Neurol. Pub Date : 2023-05-11 Frederik Thal Jantzen,Rune Häckert Christensen,Basit Ali Chaudhry,Faisal Mohammad Amin
Antibodies blocking the calcitonin gene-related peptide have revolutionized episodic and chronic migraine treatment. However, their applicability to non-cephalic pain conditions, such as osteoarthritis, is yet unknown. Osteoarthritis remains a clinical challenge, associated with high disability and limited treatment options. Like migraine, neuropeptides including calcitonin gene-related peptides are
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Sustained, Effortless Weight Loss after Damage to the Left Frontoinsular Cortex: A Case Report Case Rep. Neurol. Pub Date : 2023-03-28 Benjamin D. Reasoner, Aaron D. Boes, Joel C. Geerling
This case report highlights a possible consequence of damage to the left frontoinsular region. A 53-year-old woman with chronic obesity and headaches presented with seizure, leading to the discovery and resection of a large sphenoid wing meningioma. Postoperative brain imaging revealed loss of the left frontoinsular cortex and portions of the underlying white matter, claustrum, and striatum. Throughout
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Delayed Nonarteritic Posterior Ischemic Optic Neuropathy Following Herpes Zoster Ophthalmicus: A Case Report Case Rep. Neurol. Pub Date : 2023-03-24 Cheng-En Wu, Kuo-Hung Wen, Chin-Wei Huang
Posterior ischemic optic neuropathy (PION), a relatively rare condition, is diagnosed primarily based on the clinical presentation of sudden visual impairment, an optic nerve-related visual field defect, and an initial normal optic disc that corresponds to its pathology of acute ischemia. Among its etiologies, nonarteritic PION is one of the most common causes. Studies on cases of PION associated with
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Efficacy of Intravenous Immunoglobulins against Chronic Lymphocytic Inflammation with Pontine Perivascular Enhancement Responsive to Steroids: A Case Report Case Rep. Neurol. Pub Date : 2023-03-15 Takumi Tsuchida, Shigehisa Ura, Ichiro Yabe
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (CLIPPERS) is an inflammatory disease of the central nervous system that predominantly affects the brainstem. Apart from corticosteroids, there are few reported treatment options for CLIPPERS, and there is no standard therapy. A 77-year-old man presented with diplopia that had persisted for 5 months. Dysarthria
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Olfactory Dysfunction, an Often Neglected Symptom of Hydrocephalus: Experience from a Case of Late-Onset Idiopathic Aqueductal Stenosis Case Rep. Neurol. Pub Date : 2023-03-01 Naoya Yamazaki, Takafumi Hasegawa, Kensuke Ikeda, Ako Miyata, Shin-ichiro Osawa, Kuniyasu Niizuma, Shigenori Kanno, Teiji Tominaga, Masashi Aoki
Disturbance of smell is often accompanied with common neurodegenerative diseases such as Parkinson’s and Alzheimer’s diseases. In addition, patients with head trauma, intracranial tumors, and hydrocephalus can also develop olfactory dysfunction, and some of which can improve with treatment of the underlying disease. In clinical practice, few patients complain of smell disturbances, thus olfactory dysfunction
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A recurrent Pleomorphic Xanthoastrocytoma in the cerebellum in a young adult: A case report and review of the literature. Case Rep. Neurol. Pub Date : 2023-02-17 Ruba Aljendi, Mohammed Amr Knifaty, Mohammed Amin, Souliman Diab, Muhammad Saleh Ali, Zuheir Alshehabi
Pleomorphic xanthoastrocytoma (PXA) is a rare glioma. It accounts for less than 1% of all astrocytomas. About 98% of PXAs originate supratentorially with the temporal lobe being the most common location. Cases of infratentorial PXAs are rarely reported in the medical literature. The tumor presents with a wide variation of symptoms based on the neuroanatomy involved with the location and size of the
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An Autopsy Case of Elderly Onset Brainstem Acute Disseminated Encephalomyelitis Case Rep. Neurol. Pub Date : 2023-02-14 Yasuyuki Takai, Shinsuke Tobisawa, Asuka Funai, Takashi Komori, Kazushi Takahashi
Acute disseminated encephalomyelitis (ADEM), which is a disease that causes multifocal inflammatory demyelination of the central nervous system, occurs predominantly in children and young adults. We report an autopsy case of an elderly man with brainstem ADEM that progressed over a period of about 3 months. An 82-year-old man developed disturbance of consciousness, dysphagia, and ataxic gait over a
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Hypoglycemic Encephalopathy Manifesting with Cortical Hemichorea-Hemiballismus Syndrome: A Case Report Case Rep. Neurol. Pub Date : 2023-02-07 Francesco Pasini, Aristotelis Karantzoulis, Gaia Fanella, Francesco Brovelli, Davide Iacobucci, Vittoria Aprea, Benedetta Storti, Francesco Santangelo, Francesco Canonico, Paolo Remida, Carlo Ferrarese, Laura Brighina
Hyper-/hypoglycemic states are rare but well-established causes of hyperkinetic movements, including chorea and ballismus, usually associated with brain lesions in the basal ganglia. We report a case of hemichorea-hemiballismus (HCHB) syndrome that developed after a severe hypoglycemic episode in a 71-year-old man with poorly controlled type 2 diabetes mellitus. Uncommonly, brain MRI showed contralateral
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Hypoglycemic Encephalopathy Manifesting with Cortical Hemichorea-Hemiballismus Syndrome: A Case Report Case Rep. Neurol. Pub Date : 2023-02-07
Hyper-/hypoglycemic states are rare but well-established causes of hyperkinetic movements, including chorea and ballismus, usually associated with brain lesions in the basal ganglia. We report a case of hemichorea-hemiballismus (HCHB) syndrome that developed after a severe hypoglycemic episode in a 71-year-old man with poorly controlled type 2 diabetes mellitus. Uncommonly, brain MRI showed contralateral
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COVID-19-Associated Cerebrovascular Events: A Case Series Study and a Literature Review of Possible Mechanisms Case Rep. Neurol. Pub Date : 2023-02-03 Mostafa Meshref, Ibrahim M. Hewila, Yahia Khlidj, Rafik Korissi, Nour Shaheen, Abdulqadir J. Nashwan, Yassamine Ouerdane, Yara Amro, Khaled M. Taher, Mahmoud Galal Ahmed
Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) affects multiple body systems, including the nervous system. Cerebrovascular accidents can also occur. Patients with comorbid illnesses have severe manifestations and poor outcomes. Despite the proper mechanism of SARS-CoV-2 infection-associated stroke having not yet been settled, various possible mechanisms have been hypothesized. One possibility
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COVID-19-Associated Cerebrovascular Events: A Case Series Study and a Literature Review of Possible Mechanisms Case Rep. Neurol. Pub Date : 2023-02-03
Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) affects multiple body systems, including the nervous system. Cerebrovascular accidents can also occur. Patients with comorbid illnesses have severe manifestations and poor outcomes. Despite the proper mechanism of SARS-CoV-2 infection-associated stroke having not yet been settled, various possible mechanisms have been hypothesized. One possibility
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Small Fiber Neuropathy Triggered by COVID-19 Vaccination: Association with FGFR3 Autoantibodies and Improvement during Intravenous Immunoglobulin Treatment Case Rep. Neurol. Pub Date : 2023-01-27 Maria Mastropaolo, M. Joshua Hasbani
Multiple case series have demonstrated the emergence of small fiber neuropathy following acute coronavirus disease 2019 (COVID-19) infections. Further, one large case supports that the COVID-19 vaccine has been reported to result in small fiber neuropathy. We report a case of a patient with confirmed small fiber neuropathy post-COVID-19 vaccination with positive FGFR3 antibodies. The effect of intravenous
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Small Fiber Neuropathy Triggered by COVID-19 Vaccination: Association with FGFR3 Autoantibodies and Improvement during Intravenous Immunoglobulin Treatment Case Rep. Neurol. Pub Date : 2023-01-27
Multiple case series have demonstrated the emergence of small fiber neuropathy following acute coronavirus disease 2019 (COVID-19) infections. Further, one large case supports that the COVID-19 vaccine has been reported to result in small fiber neuropathy. We report a case of a patient with confirmed small fiber neuropathy post-COVID-19 vaccination with positive FGFR3 antibodies. The effect of intravenous
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Flank Pain as a First Symptom of a Diffuse Midline Glioma Case Rep. Neurol. Pub Date : 2023-01-12 Burc Bassa, Achim Battmann, Eva Maria Craemer, Uta Meyding-Lamadé
Diffuse midline gliomas are a new entity in the WHO Classification of Tumors of the Central Nervous System, corresponding to grade 4 gliomas. The diagnostic pathognomonic feature is the presence of a H3K27M mutation. Although mainly seen in children, cases in adults have also been reported. The symptoms are highly variable and usually dependent on the location and extent of spinal cord compression
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Flank Pain as a First Symptom of a Diffuse Midline Glioma Case Rep. Neurol. Pub Date : 2023-01-12
Diffuse midline gliomas are a new entity in the WHO Classification of Tumors of the Central Nervous System, corresponding to grade 4 gliomas. The diagnostic pathognomonic feature is the presence of a H3K27M mutation. Although mainly seen in children, cases in adults have also been reported. The symptoms are highly variable and usually dependent on the location and extent of spinal cord compression
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Favorable Outcome with Intravenous Immunoglobulin Therapy in Late-Onset Anti-mGluR1 Encephalitis: A Case Report and Literature Review Case Rep. Neurol. Pub Date : 2023-01-05 Kento Sakashita, Katsuya Nishida, Yu Takenaka, Ichiro Yokota, Hiroshi Yamasaki, Keisuke Nishimoto, Kunihiko Kawamoto, Maki Mitani, Itaru Funakawa, Nobuaki Yoshikura, Akio Kimura, Takayoshi Shimohata, Naonobu Futamura
Anti-metabotropic glutamate receptor 1 (mGluR1) encephalitis is a rare autoimmune disorder manifesting with cerebellar syndrome. Patients with mGluR1 encephalitis have been treated with immunomodulatory therapies; however, little is known about the efficacy of this therapy. A 58-year-old Japanese woman presented with dizziness when walking and standing up. Symptoms persisted and the patient gradually
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Favorable Outcome with Intravenous Immunoglobulin Therapy in Late-Onset Anti-mGluR1 Encephalitis: A Case Report and Literature Review Case Rep. Neurol. Pub Date : 2023-01-05
Anti-metabotropic glutamate receptor 1 (mGluR1) encephalitis is a rare autoimmune disorder manifesting with cerebellar syndrome. Patients with mGluR1 encephalitis have been treated with immunomodulatory therapies; however, little is known about the efficacy of this therapy. A 58-year-old Japanese woman presented with dizziness when walking and standing up. Symptoms persisted and the patient gradually
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Acknowledgement to Reviewers Case Rep. Neurol. Pub Date : 2022-12-16
Case Rep Neurol 2022;14:491–493
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Acknowledgement to Reviewers Case Rep. Neurol. Pub Date : 2022-12-16
Case Rep Neurol 2022;14:491–493
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Ischemic Optic Neuropathy Secondary to Varicella-Zoster Vasculitis Mimicking Giant Cell Arteritis: Case Report Case Rep. Neurol. Pub Date : 2022-12-05
Differentiating GCA from its many mimickers remains a challenge in the daily clinical practice, especially in patients presenting with unspecific manifestations. We present the case of an 82-year-old woman who presented with a 3-week history of left eye vision loss secondary to bilateral edema and hemorrhage of the optic discs. Despite negative bilateral temporal artery biopsies, the elevation of the
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Ischemic Optic Neuropathy Secondary to Varicella-Zoster Vasculitis Mimicking Giant Cell Arteritis: Case Report Case Rep. Neurol. Pub Date : 2022-12-05
Differentiating GCA from its many mimickers remains a challenge in the daily clinical practice, especially in patients presenting with unspecific manifestations. We present the case of an 82-year-old woman who presented with a 3-week history of left eye vision loss secondary to bilateral edema and hemorrhage of the optic discs. Despite negative bilateral temporal artery biopsies, the elevation of the
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Unilateral C1 Posterior Arch Screw-C2 Laminar Screw Posterior Fixation for Vertebral Artery Preservation in Bow Hunter’s Syndrome Case Rep. Neurol. Pub Date : 2022-11-28
Pedicle or lateral mass screws, which are usually used to fix atlantoaxial instability, increase the risk of vertebral artery (VA) injury in patients with bone or arterial anomalies or osteoporotic bone. Here, we report the use of a unilateral C1 posterior arch screw-C2 laminar screw posterior fixation with a contralateral C1 lateral mass screw for VA preservation in a patient with bow hunter’s syndrome
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Cetuximab-Induced Aseptic Meningitis in a Patient with Colorectal Cancer: A Case Report and Review of Literature Case Rep. Neurol. Pub Date : 2022-11-28 Jakob Jäger, Maximilian Sprügel, Tamara Brunner, Martin Uhl, Stefan Schwab, Francesco Vitali, Axel Wein, Bastian Volbers
Cetuximab is a chimeric IgG1 monoclonal antibody against epidermal growth factor receptor. It is approved by the European medical agency for the treatment of RAS wild-type metastatic colorectal cancer and metastatic squamous cell cancer of the head and neck. Few cases of aseptic meningitis, primarily associated with the first administration of cetuximab in patients with squamous cell cancer, have been
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Unilateral C1 Posterior Arch Screw-C2 Laminar Screw Posterior Fixation for Vertebral Artery Preservation in Bow Hunter’s Syndrome Case Rep. Neurol. Pub Date : 2022-11-28
Pedicle or lateral mass screws, which are usually used to fix atlantoaxial instability, increase the risk of vertebral artery (VA) injury in patients with bone or arterial anomalies or osteoporotic bone. Here, we report the use of a unilateral C1 posterior arch screw-C2 laminar screw posterior fixation with a contralateral C1 lateral mass screw for VA preservation in a patient with bow hunter’s syndrome
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Cetuximab-Induced Aseptic Meningitis in a Patient with Colorectal Cancer: A Case Report and Review of Literature Case Rep. Neurol. Pub Date : 2022-11-28
Cetuximab is a chimeric IgG1 monoclonal antibody against epidermal growth factor receptor. It is approved by the European medical agency for the treatment of RAS wild-type metastatic colorectal cancer and metastatic squamous cell cancer of the head and neck. Few cases of aseptic meningitis, primarily associated with the first administration of cetuximab in patients with squamous cell cancer, have been
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Unilateral C1 Posterior Arch Screw-C2 Laminar Screw Posterior Fixation for Vertebral Artery Preservation in Bow Hunter's Syndrome. Case Rep. Neurol. Pub Date : 2022-11-28 Tatsuya Tanaka,Ren Fujiwara,Haruki Funao,Shigeto Ebata,Ryohei Sashida,Yu Hirokawa,Tomihiro Wakamiya,Yuhei Michiwaki,Kazuaki Shimoji,Eiichi Suehiro,Keisuke Onoda,Fumitaka Yamane,Ken Ishii,Masatou Kawashima,Akira Matsuno
Pedicle or lateral mass screws, which are usually used to fix atlantoaxial instability, increase the risk of vertebral artery (VA) injury in patients with bone or arterial anomalies or osteoporotic bone. Here, we report the use of a unilateral C1 posterior arch screw-C2 laminar screw posterior fixation with a contralateral C1 lateral mass screw for VA preservation in a patient with bow hunter's syndrome
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Vestibular Schwannoma Presenting as Acute Vertigo Mimicking Vestibular Neuritis Case Rep. Neurol. Pub Date : 2022-11-22 Joon Yong Park, Chang-Hee Kim
Vestibular schwannoma (VS) is commonly accompanied by hearing loss, tinnitus, and dizziness and tends to be chronically progressive in nature. We report a case of VS presenting as left vestibular neuritis (VN) in a previously healthy 57-year-old patient. Right-beating horizontal-torsional spontaneous nystagmus was observed, and the bedside head impulse test revealed a left catch-up saccade. The bithermal
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Vestibular Schwannoma Presenting as Acute Vertigo Mimicking Vestibular Neuritis Case Rep. Neurol. Pub Date : 2022-11-22
Vestibular schwannoma (VS) is commonly accompanied by hearing loss, tinnitus, and dizziness and tends to be chronically progressive in nature. We report a case of VS presenting as left vestibular neuritis (VN) in a previously healthy 57-year-old patient. Right-beating horizontal-torsional spontaneous nystagmus was observed, and the bedside head impulse test revealed a left catch-up saccade. The bithermal
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Case Report: Three Case Reports of Rapidly Progressive Dementias and Narrative Review Case Rep. Neurol. Pub Date : 2022-11-11 Carlos Andrés Clavijo, Ana María Portilla Buenaventura, Galo Santiago Benavides Albornoz, Juan José Muñoz Cabrera, María Camila Murillo Reyes, Alejandra Chauvez Gallego, Carlos Alberto Hurtado González, Sebastian Ospina Otalvaro, Carlos Steven Marmolejo Escobar, Karen Julieth Quebrada Mera, Paola Andrea Gutiérrez Lenis, Lina María Arango García, Armando Lucumí
Rapidly progressive dementia (RPD) is a heterogeneous group of diseases characterized by cognitive impairment and other neurological disorders developed in a short span of fewer than 2 years. Currently viewed as new and infrequent entities, most medical personnel have little understanding of it. Nevertheless, they significantly compromise many patients’ quality of life. Here, we drive 3 clinical cases
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Rhabdomyolysis after COVID-19 Comirnaty Vaccination: A Case Report Case Rep. Neurol. Pub Date : 2022-11-04
Rhabdomyolysis is an acute disruption in skeletal muscle integrity, leading to the rapid release of 4 muscle contents into the bloodstream, such as creatine kinase (CK). It can have various causes, including infections. Throughout the pandemic, multiple cases of rhabdomyolysis following COVID-19 infections have been reported. However, rhabdomyolysis subsequent to COVID-19 vaccinations appears to be
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Multiple Endovascular Treatments for Hemorrhagic Cerebral Proliferative Angiopathy: A Case Report Case Rep. Neurol. Pub Date : 2022-11-04
Cerebral proliferative angiopathy (CPA) is a rare vascular abnormality characterized by transdural supply, stenoses of feeding arteries, and intermingled normal brain parenchyma in abnormal vessels. CPA is often regarded as a separate entity from “classical” brain arteriovenous malformations in angioarchitecture, natural history, clinical presentation, and treatment. Bleeding from CPA is uncommon,
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Rhabdomyolysis after COVID-19 Comirnaty Vaccination: A Case Report Case Rep. Neurol. Pub Date : 2022-11-04 Veerle J. Ruijters, Marjon F.G. van der Meulen, Michael A. van Es, Tessa Smit, Jessica E. Hoogendijk
Rhabdomyolysis is an acute disruption in skeletal muscle integrity, leading to the rapid release of 4 muscle contents into the bloodstream, such as creatine kinase (CK). It can have various causes, including infections. Throughout the pandemic, multiple cases of rhabdomyolysis following COVID-19 infections have been reported. However, rhabdomyolysis subsequent to COVID-19 vaccinations appears to be
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Multiple Endovascular Treatments for Hemorrhagic Cerebral Proliferative Angiopathy: A Case Report Case Rep. Neurol. Pub Date : 2022-11-04 Keijiro Shomura, Tomoya Kamide, Kouichi Misaki, Taishi Tsutsui, Iku Nambu, Naoyuki Uchiyama, Mitsutoshi Nakada
Cerebral proliferative angiopathy (CPA) is a rare vascular abnormality characterized by transdural supply, stenoses of feeding arteries, and intermingled normal brain parenchyma in abnormal vessels. CPA is often regarded as a separate entity from “classical” brain arteriovenous malformations in angioarchitecture, natural history, clinical presentation, and treatment. Bleeding from CPA is uncommon,
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Rapid Change in Shape of Unruptured Intracranial Aneurysm with Acute Perforating Infarction Case Rep. Neurol. Pub Date : 2022-10-31 Tatsuya Tanaka, Hirofumi Goto, Nobuaki Momozaki, Eiichiro Honda
Acute ischemic stroke is a rare complication resulting from an unruptured intracranial aneurysm (UIA). Ischemic stroke adjacent to the aneurysms is considered the risk of rupture of aneurysms. However, there is presently no consensus on the optimal strategy for the management of UIAs with ischemic stroke. A 27-year-old woman presented with sudden onset left hemiparesis. Acute infarction of the right
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Multiple Dural Arteriovenous Fistulas as the Mystery of Rapidly Progressive Dementia with Bilateral Thalamic Lesions Case Rep. Neurol. Pub Date : 2022-10-31 Yu Zhan, Murad Al-Nusaif, Chang Xu, Jiahao Li, Li Zhao, Feng Wang, Chunbo Dong
Dementia is a gradual and irreversible loss of higher mental function, particularly memory. Dural arteriovenous fistulas (DAVFs) are one of the rare causes of a rapid decline in cognitive function, which can be curable. DAVFs are pathological shunts between the dural artery and the dural venous sinus, dural vein, or cortical vein. Here, we present a case that initially manifested nausea and dizziness
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Serial Magnetic Resonance Imaging and Magnetic Resonance Angiographic Findings of Reversible Cerebral Vasoconstriction Syndrome Associated with Postpartum Case Rep. Neurol. Pub Date : 2022-10-31 Yumiko Nakano, Shunya Fujiwara, Yoshio Omote, Motonori Takamiya, Hisashi Narai, Yasuhiro Manabe
We report 2 cases of reversible cerebral vasoconstriction syndrome (RCVS) associated with postpartum. In case 1, a 26-year-old woman developed sudden-onset headache, nausea, and vomiting 1 h after an uncomplicated vaginal delivery. In case 2, a 27-year-old woman developed generalized seizures 9 days after an uncomplicated vaginal delivery. In both cases, initial angiographic studies showed no significant
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The Importance of F-Wave Patterns in a Patient with Cerebrovascular Disease Characterized by a Markedly Increased Tone of the Thenar Muscles Case Rep. Neurol. Pub Date : 2022-10-31 Toshiaki Suzuki, Yuki Fukumoto, Marina Todo, Makiko Tani, Sohei Yoshida
F-waves are used to measure the excitability of spinal motor nerve function. This study aimed to investigate the F-wave patterns in a patient with cerebrovascular disease who had no voluntary movement of the hand, particularly the thumb, caused by a considerably increased tone of the thenar muscles. A patient with right hemiplegia caused by left cerebral hemorrhage (putamen) showed a considerably increased