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Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon–Lefèvre syndrome: A report on two cases
Frontiers in Pediatrics ( IF 2.6 ) Pub Date : 2022-09-20 , DOI: 10.3389/fped.2022.953033
Suprit Basu 1 , Reva Tyagi 1 , Ankur Kumar Jindal 1 , Apurva Medha 1 , Aaqib Zaffar Banday 1 , Alisha Babbar 1 , Apoorva Sharma 2 , Rahul Mahajan 2 , Pandiarajan Vignesh 1 , Amit Rawat 1
Affiliation  

Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic granulomatous disease (CGD) has not been reported previously. Here, we report 2 cases of liver abscess in PLS that responded to corticosteroids.



中文翻译:

病例报告:皮质类固醇作为治疗 Papillon-Lefèvre 综合征肝脓肿的辅助治疗:两例报告

Papillon-Lefèvre 综合征 (PLS) 是一种罕见的常染色体隐性遗传疾病,临床特征为掌跖角化病、牙周炎和反复化脓性感染。患者很少报告肝脓肿。以前没有报道使用皮质类固醇治疗类似于慢性肉芽肿病 (CGD) 的肝脓肿。在这里,我们报告了 2 例对皮质类固醇有反应的 PLS 肝脓肿病例。

更新日期:2022-09-20
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