Transposition of the great arteries is the most common cyanotic CHD in newborns. This CHD, in which the aorta arises from the right ventricle and the pulmonary artery from the left ventricle, is often accompanied by one or several defects such as atrial septal defect or patent foramen ovale, ventricular septal defect and patent ductus arteriosus, which allow the transition between both parallel circulations. Rarely, the disease may be accompanied by left ventricular outflow tract obstruction (subpulmonary obstruction) and coarctation of the aorta.

We present a highly complicated and unusual transposition of the great arteries patient with critical aortic coarctation and hypoplastic pulmonary arteries with abnormal outflow and course.

大动脉转位是新生儿最常见的紫绀型先心病。这种主动脉起自右心室、肺动脉起自左心室的先心病，常伴有房间隔缺损或卵圆孔未闭、室间隔缺损、动脉导管未闭等一种或几种缺损，使两个平行循环之间的过渡。极少数情况下，该疾病可能伴有左心室流出道阻塞（肺下阻塞）和主动脉缩窄。

我们提出了一个非常复杂和不寻常的大动脉转位患者，伴有严重的主动脉缩窄和发育不全的肺动脉，伴有异常的流出和走行。