Background

Women with Mullerian agenesis, also known as Mayer-Rokitansky-Küster-Hauser syndrome (MRKH), have aplasia or hypoplasia of the uterus and vagina. Regular use of dilators can successfully create a functional vagina in up to 95% of cases. We present 3 women with Mullerian agenesis who failed dilation therapy due to pain and were subsequently found to have hymenal anomalies.

Cases

Patients presented at age 16 or 17 to initiate dilation. Initial attempts were discontinued due to pain. On examination, a septate hymen was identified in 2 patients and a microperforate hymen in 1 patient. All patients underwent hymenectomy and thereafter continued dilation with less discomfort.

Summary and Conclusion

These cases illustrate the importance of recognizing and treating hymenal anomalies in women with Mullerian agenesis to prevent pain, leading to unsuccessful dilation.

中文翻译：

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处女膜异常干扰苗勒管发育不全女性的扩张：病例系列

背景

患有苗勒管发育不全的女性，也称为 Mayer-Rokitansky-Küster-Hauser 综合征 (MRKH)，患有子宫和阴道发育不全或发育不全。在高达 95% 的情况下，经常使用扩张器可以成功地创建功能性阴道。我们介绍了 3 名患有苗勒氏管发育不全的女性，她们因疼痛而导致扩张治疗失败，随后被发现有处女膜异常。

案例

患者在 16 岁或 17 岁时开始扩张。由于疼痛，最初的尝试停止了。经检查，2 名患者发现分隔处女膜，1 名患者发现微穿孔处女膜。所有患者都接受了处女膜切除术，然后继续扩张，不适感减轻。

总结与结论

这些病例说明了识别和治疗苗勒氏管发育不全女性的处女膜异常以防止疼痛导致扩张失败的重要性。