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Malignant Pigmented Epithelioid Angiomyolipoma of the Kidney in a Child with Tuberous Sclerosis Complex
Fetal and Pediatric Pathology ( IF 1.1 ) Pub Date : 2022-06-23 , DOI: 10.1080/15513815.2022.2088911
Thu Dang Anh Phan 1 , Nhi Thuy To 2 , Diem Thi Nhu Pham 1
Affiliation  

Abstract

Introduction: Pigmented epithelioid angiomyolipoma is a variant of epithelioid angiomyolipoma (EAML) that has not previously been described in children with tuberous sclerosis.

Case presentation: A 15-year-old boy with tuberous sclerosis had a rapidly enlarging renal mass associated with a left lung nodule. Microscopically it was a pigmented EAML, confirmed by immunohistochemistry.

Discussion/Conclusion: The pigmented variant of EAML can arise and metastasize from the kidney of a teenager with tuberous sclerosis.



中文翻译:

结节性硬化症儿童肾脏恶性色素上皮样血管平滑肌脂肪瘤

摘要

简介:色素上皮样血管平滑肌脂肪瘤是上皮样血管平滑肌脂肪瘤 (EAML) 的一种变体,以前在结节性硬化症儿童中未见报道。

病例介绍:一名患有结节性硬化症的 15 岁男孩的肾脏肿块迅速增大,并伴有左肺结节。在显微镜下它是一种有色 EAML,通过免疫组织化学证实。

讨论/结论:EAML 的色素变体可以从患有结节性硬化症的青少年的肾脏出现并转移。

更新日期:2022-06-23
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