Abstract

Objective: Congenital segmental intestinal dilatation (SID) and bronchogenic cyst in the abdomen are two uncommon and different pathologies. We report a bronchogenic cyst associated with segmental intestinal dilatation. Case: A 2-day-old 3300 g term infant developed bilious vomiting. A jejunoileal segment with a diameter of 10 cm was detected at surgery. Histologically, the wall musculature and enteric plexus of the segmentally enlarged small intestine stained normally for CD117 and negative for calretinin. A bronchogenic cyst of 3 cm in diameter was centered on the mesenteric border of the dilated intestine. Conclusion: SID has a normal staining pattern for CD117 (for interstitial cells of Cajal) and negative for calretinin. it would suggest that the innervation is defective, may be associated with a bronchogenic cyst in the newborn, causing obstruction, requiring surgery.

摘要

目的：先天性节段性肠扩张 (SID) 和腹部支气管囊肿是两种不常见且不同的病理。我们报告了与节段性肠扩张相关的支气管囊肿。案例：一名出生 2 天、体重 3300 克的足月婴儿出现胆汁性呕吐。在手术中检测到直径为 10 厘米的空回肠段。组织学上，节段性扩大的小肠的壁肌肉组织和肠丛对 CD117 染色正常，对 calretinin 染色呈阴性。直径 3 cm 的支气管囊肿位于扩张肠的肠系膜边界的中心。结论：SID 具有正常的 CD117 染色模式（对于 Cajal 的间质细胞）和钙调蛋白阴性。提示神经支配有缺陷，可能与新生儿支气管囊肿有关，造成梗阻，需要手术治疗。