当前位置: X-MOL 学术Ophthalmic Plast. Reconstr. Surg. › 论文详情
Our official English website, www.x-mol.net, welcomes your feedback! (Note: you will need to create a separate account there.)
Pediatric Subcutaneous Panniculitis-like T-cell Lymphoma of the Orbit.
Ophthalmic Plastic and Reconstructive Surgery ( IF 2 ) Pub Date : 2021-10-13 , DOI: 10.1097/iop.0000000000002075
Jessica Y Tong 1, 2, 3 , Madeleine Powys 4 , Tracey Phan 1 , Michael Krivanek 5 , Stewart J Kellie 4, 6 , Krishna Tumuluri 1, 2, 3
Affiliation  

Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare and distinct subtype of peripheral T-cell lymphoma, representing <1% of all non-Hodgkin lymphomas. SPTCL usually arises in the fourth decade of life with multifocal involvement of the limbs and trunk. Orbital disease is uncommon. We present the youngest known case of orbital SPTCL in a 3-year-old child, where the diagnosis was initially confounded by a lower eyelid mass masquerading as preseptal cellulitis. MRI revealed a poorly defined anterior orbital mass. Immunophenotyping and histological analysis of an orbital biopsy specimen confirmed SPTCL, which was managed by the pediatric oncology team with multiagent chemotherapy. This case is unique due to the young age of presentation and primary orbital involvement. Nonresolving or atypical periorbital cellulitis needs to be investigated, as malignancy can mimic such conditions.

中文翻译:

小儿皮下脂膜炎样眼眶 T 细胞淋巴瘤。

皮下脂膜炎样 T 细胞淋巴瘤 (SPTCL) 是一种罕见且独特的外周 T 细胞淋巴瘤亚型,占所有非霍奇金淋巴瘤的 <1%。SPTCL 通常发生在四十岁左右,四肢和躯干多灶性受累。眼眶疾病并不常见。我们介绍了已知最年轻的眼眶 SPTCL 病例,患者为一名 3 岁儿童,最初因伪装成房间隔蜂窝织炎的下眼睑肿块而混淆了诊断。MRI 显示前眼眶肿块边界不清。眼眶活检标本的免疫表型和组织学分析证实了 SPTCL,该病由儿科肿瘤团队采用多药化疗进行治疗。由于发病年龄小且主要眼眶受累,该病例是独一无二的。需要对未缓解或非典型的眶周蜂窝织炎进行研究,因为恶性肿瘤可能会模仿此类情况。
更新日期:2021-10-13
down
wechat
bug