Carney complex is a rare syndrome caused by a genetic mutation leading to multiple endocrine abnormalities and a variety of tumors. Here, we report a case of Carney complex diagnosed due to recurrent multiple myxomas in the right atrium of a patient 16 years after the resection of the primary left atrial myxoma. Surgical excision was performed for the multiple recurrent right atrial tumors under cardiopulmonary bypass. The patient remained complication-free after surgery and was discharged on the 14th day. He was scheduled to continue echocardiographic follow-up and periodic systemic review by an endocrinologist. This case emphasizes the fact that if cardiac myxomas tend to be multiple and recurrent at a relatively young age, the possibility of Carney complex should be considered, even in the absence of any other related feature other than cardiac tumors.

卡尼综合征是一种罕见的综合征，由基因突变导致多种内分泌异常和多种肿瘤引起。在这里，我们报告一例因原发性左心房粘液瘤切除 16 年后患者右心房复发性多发性粘液瘤而诊断为 Carney 复合体的病例。体外循环下对多发性右心房肿瘤进行手术切除。术后患者无并发症，第14天出院。他计划继续由内分泌学家进行超声心动图随访和定期系统检查。该病例强调，如果心脏粘液瘤往往多发且在相对年轻时复发，则应考虑卡尼复合体的可能性，