Cystic fibrosis (CF) was historically a disease largely afflicting children. Due to therapeutic advancements, there are now more adults with CF than children. In the past decade, medications including Cystic Fibrosis Transmembrane conductance Regulator (CFTR) modulators became available that treat the underlying cause of CF and are dramatically improving lung function as well as quality and quantity of life for people with CF. As a result, more women with CF are becoming pregnant. We gathered a panel of experts in CF care, family planning, high risk obstetrics, nutrition, genetics and women with CF to review current literature on pregnancies and to provide care recommendations for this unique population.

囊性纤维化 (CF) 在历史上是一种主要困扰儿童的疾病。由于治疗的进步，现在患有 CF 的成年人比儿童多。在过去十年中，包括囊性纤维化跨膜电导调节剂 (CFTR) 调节剂在内的药物问世，可治疗 CF 的根本原因，并显着改善 CF 患者的肺功能以及生活质量和数量。结果，越来越多的患有 CF 的女性怀孕了。我们召集了一个由 CF 护理、计划生育、高危产科、营养、遗传学和 CF 女性组成的专家小组，回顾当前有关怀孕的文献，并为这一独特人群提供护理建议。