Situs inversus totalis (SIT) is an extremely uncommon congenital disease where the major organs of the body are transposed through the sagittal plane. Kartagener syndrome is a complication of SIT with immotility of bronchial cilia, bronchiectasis, and chronic sinusitis. There is no report describing patients with Kartagener syndrome who accept uni-portal segmentectomies for lung cancer in past studies. Here we report a 74-year-old female patient with both Kartagener syndrome and a small early-stage lung cancer lesion located in the apical segment of the left upper lobe (LS¹). The pulmonary segment anatomy of the left upper lobe in this case, which had very rare variants, was presented and interpreted in detail. This patient underwent an anatomic segmentectomy to the LS¹ and a partial excision to the left middle lobe with bronchiectasis through a single 3 cm length incision. We believe that the case can give surgeons some experience and inspiration.

全内翻（SIT）是一种极其罕见的先天性疾病，身体的主要器官通过矢状面移位。Kartagener 综合征是 SIT 的并发症，伴有支气管纤毛不活动、支气管扩张和慢性鼻窦炎。在过去的研究中，没有报道描述接受单门肺段切除术治疗肺癌的 Kartagener 综合征患者。在这里，我们报告了一名 74 岁的女性患者，同时患有 Kartagener 综合征和位于左上叶 (LS ¹ ) 心尖段的早期肺癌小病灶。本例中左上叶的肺段解剖结构非常罕见，其变异非常罕见，被详细介绍和解释。该患者接受了 LS ^{1的解剖性肺段切除术}通过一个 3 cm 长的切口部分切除伴有支气管扩张的左中叶。我们相信这个案例能给外科医生一些经验和启示。