Aim:

To synthesize published evidence regarding hearing impairment diagnosis and interventions in infants with or at high risk for cerebral palsy in the first year after birth.

Method:

Nine databases were searched for MeSH terms up to February 2020. Included studies were published in English, enrolled infants with or at high risk for cerebral palsy, and addressed hearing evaluation/rehabilitation within the first year after birth. Quality of evidence was evaluated using RTI Item Bank and QUADAS-2.

Results:

Eighteen articles met inclusion criteria. Quality of the evidence ranged from low to high, revealing variability in diagnostic assessment methodologies and adherence to diagnostic schedules. Concerns for bias included lack of recognition of cerebral palsy effects and etiologies on functional hearing assessment methods and results. Two interventions (hearing aid and cochlear implantation) were identified; however, reported use was inconsistent.

Interpretation:

Hearing screening in infants with or at high risk for cerebral palsy requires evaluation of the entire auditory pathway preferentially using comprehensive electrophysiological panels of assessments. For infants with perinatal neural insults, pediatric neurologists are uniquely positioned to recommend adherence to systematic surveillance and comprehensive audiology assessments, regardless of comorbidities and motor impairments.

中文翻译：

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脑瘫或脑瘫高危婴儿的听力损失诊断和早期听力相关干预：系统评价

目的：

综合已发表的关于出生后第一年脑瘫或脑瘫高危婴儿的听力障碍诊断和干预措施的证据。

方法：

截至 2020 年 2 月，在九个数据库中搜索了 MeSH 术语。纳入的研究以英文发表，纳入患有脑瘫或脑瘫高风险的婴儿，并在出生后第一年内进行听力评估/康复。使用 RTI 项目库和 QUADAS-2 评估证据质量。

结果：

十八篇文章符合纳入标准。证据的质量从低到高不等，揭示了诊断评估方法的可变性和对诊断时间表的遵守情况。对偏见的担忧包括缺乏对功能性听力评估方法和结果的脑瘫影响和病因的认识。确定了两种干预措施（助听器和人工耳蜗植入）；然而，报告的使用情况并不一致。

解释：

脑瘫或脑瘫高危婴儿的听力筛查需要优先使用综合电生理评估小组来评估整个听觉通路。对于患有围产期神经损伤的婴儿，儿科神经科医生具有独特的优势，可以建议坚持系统监测和全面的听力学评估，无论合并症和运动障碍如何。