Subacute sclerosing panencephalitis (SSPE) is a potentially lethal complication of measles infection. Neurological complications take years to manifest after primary viral infection of brain and can lead to blindness in some individuals. A 13-year-old female patient with history of Bell’s palsy 2 months prior, presented with rapidly progressing necrotizing retinitis in both eyes. Soon after, she was unable to walk, developed myoclonic jerks, altered sensorium and loss of bowel and bladder control. Her clinical history, CSF IgG measles antibody analysis, MRI brain and EEG findings confirmed the diagnosis of SSPE. SSPE in our case presented as Bell’s palsy and sudden painless diminution of vision due to ocular involvement, and developed full blown disease within 2 months. SSPE can present as a diagnostic challenge and warrants early identification and referral for timely diagnosis and management.

中文翻译：

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亚急性硬化性全脑炎表现为贝尔麻痹和双侧黄斑坏死性视网膜炎：一种非典型表现

亚急性硬化性全脑炎（SSPE）是麻疹感染的潜在致命并发症。原发性脑部病毒感染后，神经系统并发症需要数年才能显现出来，并可能导致某些人失明。一名2个月前患有贝尔麻痹病史的13岁女性患者，双眼均出现快速进展的坏死性视网膜炎。此后不久，她无法行走，发展为肌阵挛性抽搐，感觉觉改变，肠管和膀胱失去控制。她的临床病史，脑脊液IgG麻疹抗体分析，MRI脑和脑电图结果证实了SSPE的诊断。在我们的案例中，SSPE表现为由于眼部受累而引起的贝尔麻痹和视力突然无痛性减弱，并在2个月内发展为完全性疾病。