BACKGROUND The high incidence and prevalence of chronic pain in patients with cystic fibrosis (CF) is well documented. However, there is limited data on chronic pain management in this population. METHODS We designed a questionnaire examining care team members' views on the prevalence and characteristics of pain, pain management, and opioid use. The questionnaire was distributed to accredited programs throughout the US via a CF Foundation (CFF) email list-serve. RESULTS Responses came from 52 adult core or affiliated centers (Adult Responders - AR), 36 pediatric core or affiliated centers (Pediatric Responders - PR), and 9 were from combined programs. AR perceive more patients having chronic pain compared to PR. Furthermore, 40% of the AR said that > 50% of those with chronic pain also have comorbid depression or anxiety. 61% of PR ranked sinus/headache symptoms as the most common while AR ranked chest wall as the most frequent site (58%). While most centers (83%) report that pain management in patients with CF is a very important or important issue, 50% of AR feel uncomfortable or only slightly comfortable in prescribing opioids. 44% report that CF providers are currently responsible for this task. CONCLUSIONS Chronic pain is common in adult patients with CF and management presents a formidable challenge to providers. The development of guidelines and/or collaboration with pain specialists will likely benefit both patients and providers.

中文翻译：

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美国囊性纤维化中心对疼痛和阿片类药物处方实践的态度

背景 囊性纤维化 (CF) 患者慢性疼痛的高发病率和患病率已得到充分证明。然而，关于该人群慢性疼痛管理的数据有限。方法 我们设计了一份调查问卷，调查护理团队成员对疼痛、疼痛管理和阿片类药物使用的流行和特征的看法。问卷通过 CF 基金会 (CFF) 电子邮件列表服务分发给美国各地的认可项目。结果 回应来自 52 个成人核心或附属中心 (Adult Responders - AR)、36 个儿科核心或附属中心 (Pediatric Responders - PR)，9 个来自联合项目。与 PR 相比，AR 发现更多患有慢性疼痛的患者。此外，40% 的 AR 表示，> 50% 的慢性疼痛患者还患有抑郁症或焦虑症。61% 的 PR 将鼻窦/头痛症状列为最常见，而 AR 将胸壁列为最常见的部位 (58%)。虽然大多数中心 (83%) 报告说 CF 患者的疼痛管理是一个非常重要或重要的问题，但 50% 的 AR 对开阿片类药物感到不舒服或只是稍微舒服。44% 的人报告说，CF 提供者目前负责这项任务。结论 慢性疼痛在成年 CF 患者中很常见，管理对提供者来说是一项艰巨的挑战。指南的制定和/或与疼痛专家的合作可能会使患者和提供者都受益。50% 的 AR 患者在处方阿片类药物时感到不舒服或仅略微舒服。44% 的人报告说，CF 提供者目前负责这项任务。结论 慢性疼痛在成年 CF 患者中很常见，管理对提供者来说是一项艰巨的挑战。指南的制定和/或与疼痛专家的合作可能会使患者和提供者都受益。50% 的 AR 患者在处方阿片类药物时感到不舒服或仅略微舒服。44% 的人报告说，CF 提供者目前负责这项任务。结论 慢性疼痛在成年 CF 患者中很常见，管理对提供者来说是一项艰巨的挑战。指南的制定和/或与疼痛专家的合作可能会使患者和提供者都受益。