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Twiddler’s syndrome with occult lead insulation damage in a child with epicardial pacemaker leads
Cardiology in the Young ( IF 1 ) Pub Date : 2020-05-19 , DOI: 10.1017/s1047951120001031
Peter Kramer 1 , Felix Berger 1, 2, 3 , Björn Peters 1
Affiliation  

We present a rare case of incidentally diagnosed Twiddler’s syndrome in a child 7 years after implantation of a dual-chamber pacemaker system with epicardial leads. During revision, an insulation defect of the ventricular lead was evident, despite unremarkable prior pacemaker lead testing. The lead was repaired and a new generator was suture-fixated to prevent re-occurrence of generator manipulation.

中文翻译:

Twiddler 综合征伴隐匿性导线绝缘损伤的儿童心外膜起搏器导线

我们介绍了一个在植入带有心外膜导线的双腔起搏器系统后 7 年偶然诊断出的儿童 Twiddler 综合征的罕见病例。在翻修过程中,尽管先前的起搏器导联测试不显着,但心室导联的绝缘缺陷很明显。修复导线并缝合新的发电机,以防止再次发生发电机操作。
更新日期:2020-05-19
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