We report the case of a 5-year-old boy who developed chronic plastic bronchitis after Fontan surgery for a complex congenital heart disease. During a new admission for acute exacerbation of plastic bronchitis, he started on a mucolytic treatment with inhaled rhDNAse instead of inhaled fibrinolytics because of the potential bleeding risk in a patient on combined coumarin and aspirin treatment. Respiratory symptoms resolved promptly, and the patient was discharged home on rhDNAse treatment. He remained clinically stable on rhDNAse treatment without further hospitalization until definitive treatment with dynamic lymphangiography and percutaneous embolization.

中文翻译：

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人脱氧核糖核酸酶（rhDNase）雾化作为Font门手术后难治性塑性支气管炎的替代治疗。

我们报告了一个5岁男孩在Fontan手术后因复杂的先天性心脏病而患上慢性塑料性支气管炎的病例。在新入院的急性支气管炎急性加重期期间，他开始使用吸入的rhDNAse代替吸入的纤维蛋白溶解剂进行粘液溶解治疗，因为香豆素和阿司匹林联合治疗可能会导致出血风险。呼吸道症状迅速缓解，患者在进行rhDNAse治疗后出院。他在进行rhDNAse治疗后一直保持临床稳定，无需进一步住院，直到通过动态淋巴管造影术和经皮栓塞术进行彻底治疗。